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Literature summary for 3.2.1.51 extracted from

  • Kress, B.C.; Freeze, H.H.; Herd, J.K.; Alhadeff, J.A.; Miller, A.L.
    Purification and characterization of I-cell disease alpha-L-fucosidase (1980), J. Biol. Chem., 255, 955-961.
    View publication on PubMed

KM Value [mM]

KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
0.05 0.06 4-methylumbelliferyl-alpha-L-fucopyranoside
-
Homo sapiens

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Posttranslational Modification

Posttranslational Modification Comment Organism
glycoprotein altered carbohydrate composition from enzymes of liver I-cell disease or pseudo-Hurler polydystrophy urine samples Homo sapiens

Purification (Commentary)

Purification (Comment) Organism
to homogeneity, affinity chromatography Homo sapiens

Source Tissue

Source Tissue Comment Organism Textmining
liver normal and I-cell disease samples Homo sapiens
-
urine samples from pseudo-Hurler polydystrophy Homo sapiens
-

Specific Activity [micromol/min/mg]

Specific Activity Minimum [µmol/min/mg] Specific Activity Maximum [µmol/min/mg] Comment Organism
39.7
-
-
Homo sapiens

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
4-methylumbelliferyl-alpha-L-fucopyranoside + H2O
-
Homo sapiens 4-methylumbelliferone + alpha-L-fucose
-
?

pH Optimum

pH Optimum Minimum pH Optimum Maximum Comment Organism
3.9 4 major pH-optimum Homo sapiens
6.9
-
second minor pH-optimum Homo sapiens