KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.05 | 0.06 | 4-methylumbelliferyl-alpha-L-fucopyranoside | - |
Homo sapiens |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Posttranslational Modification | Comment | Organism |
---|---|---|
glycoprotein | altered carbohydrate composition from enzymes of liver I-cell disease or pseudo-Hurler polydystrophy urine samples | Homo sapiens |
Purification (Comment) | Organism |
---|---|
to homogeneity, affinity chromatography | Homo sapiens |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
liver | normal and I-cell disease samples | Homo sapiens | - |
urine | samples from pseudo-Hurler polydystrophy | Homo sapiens | - |
Specific Activity Minimum [µmol/min/mg] | Specific Activity Maximum [µmol/min/mg] | Comment | Organism |
---|---|---|---|
39.7 | - |
- |
Homo sapiens |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
4-methylumbelliferyl-alpha-L-fucopyranoside + H2O | - |
Homo sapiens | 4-methylumbelliferone + alpha-L-fucose | - |
? |
pH Optimum Minimum | pH Optimum Maximum | Comment | Organism |
---|---|---|---|
3.9 | 4 | major pH-optimum | Homo sapiens |
6.9 | - |
second minor pH-optimum | Homo sapiens |