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Literature summary for 3.2.1.46 extracted from

  • Goda, S.; Kobayashi, T.; Goto, I.
    Hydrolysis of galactosylsphingosine and lactosylsphingosine by beta-galactosidases in human brain and cultured fibroblasts (1987), Biochim. Biophys. Acta, 920, 259-265.
    View publication on PubMed

Activating Compound

Activating Compound Comment Organism Structure
Activator protein purified from normal spleen Homo sapiens
cholate
-
Homo sapiens
phosphatidylcholine from 0.02 mg to 0.1 mg Homo sapiens
phosphatidylinositol from 0.02 mg to 0.05 mg Homo sapiens
phosphatidylserine at 0.02 mg Homo sapiens
taurocholate
-
Homo sapiens

Application

Application Comment Organism
medicine enzyme deficiency in globoid cell leucodystrophy or Krabbe disease Homo sapiens

KM Value [mM]

KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
0.11
-
galactosylsphingosine without taurocholate Homo sapiens
0.67
-
galactosylsphingosine with taurocholate Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
D-galactosyl-N-acylsphingosine + H2O Homo sapiens
-
?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
brain
-
Homo sapiens
-
skin fibroblast in culture Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
D-galactosyl-N-acylsphingosine + H2O
-
Homo sapiens D-galactose + N-acylsphingosine
-
?
D-galactosyl-N-acylsphingosine + H2O
-
Homo sapiens ?
-
?
galactocerebroside + H2O
-
Homo sapiens D-galactose + N-acylceramide
-
?
lactosylsphingosine + H2O
-
Homo sapiens lactose + sphingosine
-
?
psychosine + H2O
-
Homo sapiens D-galactose + sphingosine
-
?

pH Optimum

pH Optimum Minimum pH Optimum Maximum Comment Organism
3.75
-
without taurocholate Homo sapiens
5.4
-
with taurocholate Homo sapiens