Activating Compound | Comment | Organism | Structure |
---|---|---|---|
Activator protein | purified from normal spleen | Homo sapiens | |
cholate | - |
Homo sapiens | |
phosphatidylcholine | from 0.02 mg to 0.1 mg | Homo sapiens | |
phosphatidylinositol | from 0.02 mg to 0.05 mg | Homo sapiens | |
phosphatidylserine | at 0.02 mg | Homo sapiens | |
taurocholate | - |
Homo sapiens |
Application | Comment | Organism |
---|---|---|
medicine | enzyme deficiency in globoid cell leucodystrophy or Krabbe disease | Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.11 | - |
galactosylsphingosine | without taurocholate | Homo sapiens | |
0.67 | - |
galactosylsphingosine | with taurocholate | Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
D-galactosyl-N-acylsphingosine + H2O | Homo sapiens | - |
? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
brain | - |
Homo sapiens | - |
skin fibroblast | in culture | Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
D-galactosyl-N-acylsphingosine + H2O | - |
Homo sapiens | D-galactose + N-acylsphingosine | - |
? | |
D-galactosyl-N-acylsphingosine + H2O | - |
Homo sapiens | ? | - |
? | |
galactocerebroside + H2O | - |
Homo sapiens | D-galactose + N-acylceramide | - |
? | |
lactosylsphingosine + H2O | - |
Homo sapiens | lactose + sphingosine | - |
? | |
psychosine + H2O | - |
Homo sapiens | D-galactose + sphingosine | - |
? |
pH Optimum Minimum | pH Optimum Maximum | Comment | Organism |
---|---|---|---|
3.75 | - |
without taurocholate | Homo sapiens |
5.4 | - |
with taurocholate | Homo sapiens |