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Literature summary for 1.3.8.6 extracted from

  • McClelland Verity , M.V.; Gissen Pau, G.P.; Hendriksz Chri, H.C.; Chakrapani Anupa, C.A.
    Glutaryl-CoA dehydrogenase deficiency (2007), Pediatr. Res., 61, 134-135.
No PubMed abstract available

Application

Application Comment Organism
medicine glutaryl-CoA dehydrogenase deficiency leads to strong glutaric acid and 3-hydroxyglutaric acid accumulation in the central nervous system Homo sapiens

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
glutaryl-CoA + acceptor
-
Homo sapiens crotonyl-CoA + CO2 + reduced acceptor
-
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