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Literature summary for 1.2.1.47 extracted from

  • Wen, G.; Ringseis, R.; Rauer, C.; Eder, K.
    The mouse gene encoding the carnitine biosynthetic enzyme 4-N-trimethylaminobutyraldehyde dehydrogenase is regulated by peroxisome proliferator-activated receptor alpha (2012), Biochim. Biophys. Acta, 1819, 357-365.
    View publication on PubMed

Localization

Localization Comment Organism GeneOntology No. Textmining

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
4-N-trimethylaminobutyraldehyde + NAD+ + H2O Mus musculus
-
gamma-butyrobetaine + NADH + H+
-
?

Organism

Organism UniProt Comment Textmining
Mus musculus Q9JLJ2
-
-

Source Tissue

Source Tissue Comment Organism Textmining
liver
-
Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
4-N-trimethylaminobutyraldehyde + NAD+ + H2O
-
Mus musculus gamma-butyrobetaine + NADH + H+
-
?

Synonyms

Synonyms Comment Organism
4-N-trimethylaminobutyraldehyde dehydrogenase
-
Mus musculus
TMABA-DH
-
Mus musculus

Cofactor

Cofactor Comment Organism Structure
NAD+
-
Mus musculus

Expression

Organism Comment Expression
Mus musculus the enzyme gene is activated by peroxisome proliferator-activated receptor alpha directly and by WY-14,643 in the liver of wild type mice up