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Acidosis
Effects of C1 inhibitor on tissue damage in a porcine model of controlled hemorrhage.
Acquired Immunodeficiency Syndrome
A dual role for Mannan-binding lectin-associated serine protease 2 (MASP-2) in HIV infection.
Acute Kidney Injury
A Randomized Trial of Recombinant Human C1-Esterase-Inhibitor in the Prevention of Contrast-Induced Kidney Injury.
Acute Kidney Injury
Activation of both coagulation and fibrinolysis in childhood hemolytic uremic syndrome.
Acute Kidney Injury
An Unusual Case of Acquired Angioedema and Monoclonal Gammopathy of Renal Significance in a Middle-Aged Caucasian Female.
Acute Kidney Injury
Complement Activation in Kidneys of Patients With COVID-19.
Acute Kidney Injury
Mannan-binding lectin-associated serine protease 2 is critical for the development of renal ischemia reperfusion injury and mediates tissue injury in the absence of complement C4.
Acute Kidney Injury
The Inhibition of Complement System in Formal and Emerging Indications: Results from Parallel One-Stage Pairwise and Network Meta-Analyses of Clinical Trials and Real-Life Data Studies.
Adenocarcinoma
Clinical significance of mannose-binding lectin-associated serine protease-2 expression in esophageal squamous cell carcinoma.
Airway Obstruction
C1-esterase inhibitor concentrate prevents upper airway obstruction in hereditary angio-oedema.
Airway Obstruction
Clinical studies of sudden upper airway obstruction in patients with hereditary angioedema due to C1 esterase inhibitor deficiency.
Airway Obstruction
Critical upper airway obstruction in sporadic angioedema responding to C1-esterase inhibitor.
Airway Obstruction
Treatment for hereditary angioedema with normal C1-INH and specific mutations in the F12 gene (HAE-FXII).
Airway Obstruction
[Episodes of angioedema in children with C1 esterase inhibitor deficiency]
Amyloidosis
Budgetary Impact of Medicinal Therapies for Rare Diseases in Bulgaria.
Anaphylaxis
An 82-year-old man with recurrent angioedema.
Anaphylaxis
C1 esterase inhibitor deficiency in X-linked hypogammaglobulinaemia: an anomaly fostering anaphylactoid reactions following intramuscular gammaglobulin administration.
Anaphylaxis
Chapter 25: Idiopathic anaphylaxis.
Anaphylaxis
Idiopathic anaphylaxis.
Anaphylaxis
Role of complement in a murine model of peanut-induced anaphylaxis.
Anaphylaxis
[Idiopathic anaphylaxis]
Anemia, Hemolytic
Inhibition of complement C1s improves severe hemolytic anemia in cold agglutinin disease: a first-in-human trial.
Anemia, Hemolytic, Autoimmune
Acquired C1 esterase deficiency with cold agglutinin disease associated with monoclonal IgM antibodies.
Anemia, Hemolytic, Autoimmune
C1-esterase inhibitor concentrate rescues erythrocytes from complement-mediated destruction in autoimmune hemolytic anemia.
Anemia, Hemolytic, Autoimmune
Inhibition of complement C1s improves severe hemolytic anemia in cold agglutinin disease: a first-in-human trial.
Anemia, Hemolytic, Autoimmune
Inhibition of complement C1s in patients with cold agglutinin disease: lessons learned from a named patient program.
Anemia, Hemolytic, Autoimmune
Lupus anticoagulant and thrombosis in splenic marginal zone lymphoma.
Anemia, Hemolytic, Autoimmune
TNT003, an inhibitor of the serine protease C1s, prevents complement activation induced by cold agglutinin disease patient autoantibodies.
Angina, Unstable
[Evaluation of C3c, C4 and C1-esterase inhibitor (C1-INH) during unstable angina]
Angioedema
'Epinephrine-resistant' angioedema.
Angioedema
A Case of Angioedema Due to Acquired C1 Esterase Inhibitor Deficiency Masquerading as Suspected Peritonitis: A Case Report.
Angioedema
A patient with chronic lymphocytic leukemia and acquired angioedema: correlation of clinical and biochemical response to CLL therapy.
Angioedema
Acquired Angioedema: A Rare Manifestation of Angioimmunoblastic T Cell Lymphoma.
Angioedema
Acquired angioedema: Autoantibody associations and C1q utility as a diagnostic tool.
Angioedema
Acquired angioedema: observations on the mechanism of action of autoantibodies directed against C1 esterase inhibitor.
Angioedema
Acquired C1 esterase inhibitor deficiency and angioedema: a review.
Angioedema
Acquired C1 esterase inhibitor deficiency causing intestinal angioedema: CT appearance.
Angioedema
Acquired C1 esterase inhibitor deficiency or serendipity? The chance finding of a paraprotein after an apparently low C1 esterase inhibitor concentration.
Angioedema
Acquired C1-esterase inhibitor deficiency: three case reports and commentary on the syndrome.
Angioedema
Acute upper airway angioedema secondary to acquired C1 esterase inhibitor deficiency: a case report.
Angioedema
Acute upper airway obstruction from acquired angioedema.
Angioedema
Administration of conestat alfa, human C1 esterase inhibitor and icatibant in the treatment of acute angioedema attacks in adults with hereditary angioedema due to C1 esterase inhibitor deficiency. Treatment comparison based on systematic review results.
Angioedema
Advances in basic and clinical immunology in 2009.
Angioedema
Allergic urticaria and hereditary angioedema. Independent association in the same patient.
Angioedema
An 82-year-old man with recurrent angioedema.
Angioedema
An evidence based therapeutic approach to hereditary and acquired angioedema.
Angioedema
An Unusual Case of Acquired Angioedema and Monoclonal Gammopathy of Renal Significance in a Middle-Aged Caucasian Female.
Angioedema
An update on the diagnosis and management of hereditary angioedema with abnormal c1 inhibitor.
Angioedema
Anaesthetic management of an emergency caesarean section in a complex immunologically compromised patient with pre-eclampsia and multifactorial thrombocytopaenia.
Angioedema
Angioedema and acquired C1 esterase inhibitor deficiency.
Angioedema
Angioedema as a predominant symptom of Bordetella pertussis infection.
Angioedema
Angioedema as the first presentation of B-cell non-Hodgkin lymphoma--an unusual case with normal C1 esterase inhibitor level: a case report.
Angioedema
Angioedema due to acquired C1-esterase inhibitor deficiency in a patient with Helicobacter pylori infection.
Angioedema
Angioedema due to Systemic Isotretinoin Therapy.
Angioedema
Angioedema in a patient with c1 esterase inhibitor deficiency.
Angioedema
Angioedema in pediatric heart transplant recipients-reporting C1-esterase inhibitor deficiency without analysing protein.
Angioedema
Angioedema in the emergency department: a practical guide to differential diagnosis and management.
Angioedema
Angioedema in the emergency department: a presentation of lymphoma.
Angioedema
Angioedema of the tongue due to acquired C1 esterase inhibitor deficiency.
Angioedema
Angioedema related to angiotensin-converting enzyme inhibitors.
Angioedema
Angioedema secondary to angiotensin converting enzyme inhibitors is not due to C1 esterase inhibitor deficiency.
Angioedema
Angioedema suppressed by a combination of anti-histamine and leukotriene modifier.
Angioedema
Angioedema triggered by pulp extirpation-a case report.
Angioedema
Angioedema: frightening and frustrating.
Angioedema
Angioedema: manifestations and management.
Angioedema
Angiotensin-converting enzyme inhibitor-associated angioedema treated with c1-esterase inhibitor: A case report and review of the literature.
Angioedema
Angiotensin-converting enzyme inhibitors-induced angioedema treated by C1 esterase inhibitor concentrate (Berinert®): about one case and review of the therapeutic arsenal.
Angioedema
Antiepileptic drug-induced lymphoproliferative disorder associated with acquired C1 esterase inhibitor deficiency and angioedema.
Angioedema
Autoimmune acquired form of angioedema that responded to danazol therapy.
Angioedema
C1 Esterase Inhibitor (Berinert) for ACE Inhibitor-Induced Angioedema: Two Case Reports.
Angioedema
C1 esterase inhibitor concentrate in 1085 Hereditary Angioedema attacks--final results of the I.M.P.A.C.T.2 study.
Angioedema
C1 Esterase Inhibitor for Ace-Inhibitor Angioedema: A Case Series and Literature Review.
Angioedema
C1 esterase inhibitor for angiotensin-converting enzyme inhibitor-induced angioedema at a community teaching health system: A brief retrospective propensity-matched cohort study.
Angioedema
C1 esterase inhibitor use in the management of lisinopril-induced angioedema: A case series.
Angioedema
C1 esterase inhibitor: clinical clues to the pathophysiology of angioedema.
Angioedema
C1-esterase inhibitor deficiency in pediatric heart transplant recipients: incidence and findings on ultrasound.
Angioedema
C1-esterase inhibitor transfusions in patients with hereditary angioedema.
Angioedema
Correction of recurrent angioedema related to C1 esterase inhibitor deficiency as a secondary event following nonmyeloablative allogeneic stem cell transplantation in a patient with myelofibrosis.
Angioedema
Cost-utility analysis of Ruconest(®) (conestat alfa) compared to Berinert(®) P (human C1 esterase inhibitor) in the treatment of acute, life-threatening angioedema attacks in patients with hereditary angioedema.
Angioedema
Critical upper airway obstruction in sporadic angioedema responding to C1-esterase inhibitor.
Angioedema
Does heparin prophylaxis prevent exacerbations of hereditary angioedema?
Angioedema
DX-88 and HAE: a developmental perspective.
Angioedema
Effectiveness of C1-INH therapy in angiotensin converting enzyme inhibitor induced angioedema.
Angioedema
Efficacy of Treatment of Non-hereditary Angioedema.
Angioedema
Epidemiology of Non-hereditary Angioedema.
Angioedema
Exacerbation of a lupus-erythematosus-like syndrome during treatment of non-C1-esterase-inhibitor-dependent angioedema with danazol.
Angioedema
Examination of baseline levels of carboxypeptidase N and complement components as potential predictors of angioedema associated with the use of an angiotensin-converting enzyme inhibitor.
Angioedema
Exposure-Response Model of Subcutaneous C1-Inhibitor Concentrate to Estimate the Risk of Attacks in Patients With Hereditary Angioedema.
Angioedema
Facial angioedema and systemic lupus erythematosus: case report.
Angioedema
Helicobacter pylori infection and skin diseases.
Angioedema
Hereditary and acquired angioedema: problems and progress: proceedings of the third C1 esterase inhibitor deficiency workshop and beyond.
Angioedema
Hereditary angioedema as a cause of transient abdominal pain.
Angioedema
Hereditary angioedema due to deficit of C1 esterase inhibitor.
Angioedema
Hereditary angioedema: a family study.
Angioedema
Human parvovirus infection: rheumatic manifestations, angioedema, C1 esterase inhibitor deficiency, ANA positivity, and possible onset of systemic lupus erythematosus.
Angioedema
Idiopathic nonhistaminergic angioedema successfully treated with ecallantide, icatibant, and C1 esterase inhibitor replacement.
Angioedema
Intestinal angioedema caused by an acquired C1 esterase inhibitor deficiency associated with underlying splenic marginal zone lymphoma.
Angioedema
Intractable acquired autoimmune angioedema in a patient with systemic lupus erythematosus.
Angioedema
Isolated angioedema of the bowel due to C1 esterase inhibitor deficiency: a case report and review of literature.
Angioedema
Laboratory testing for C1 inhibitor deficiency: a comparison of two approaches to C1 inhibitor function.
Angioedema
Laparoscopic splenectomy in a patient with acquired angioneurotic edema.
Angioedema
Long-standing angioedema with C1 esterase inhibitor deficiency associated with occult lymphoma.
Angioedema
Management of dental-oral procedures in patients with hereditary angioedema due to C1 inhibitor deficiency.
Angioedema
Molecular diagnosis and management of hereditary angioedema in a Greek family.
Angioedema
Monoclonal gammopathy in association with allergic disorders of the skin and respiratory tract.
Angioedema
Monoclonal gammopathy with significance: case series and literature review.
Angioedema
Non-myeloablative allogeneic stem cell transplantation: a new treatment option for acquired angioedema?
Angioedema
Off-Label Use of Agents for Management of Serious or Life-threatening Angiotensin Converting Enzyme Inhibitor-Induced Angioedema.
Angioedema
Oral medicine case book 64: Some aspects of the pathophysiology of angioedema with special reference to the upper aerodigestive tract.
Angioedema
Perioperative course in patients with hereditary or acquired angioedema.
Angioedema
Perioperative management of tooth extractions for a patient with hereditary angioedema.
Angioedema
Peripheral edema due to increased vascular permeability: a clinical appraisal.
Angioedema
Prognostic factors in outcome of angioedema in the emergency department.
Angioedema
Recurrent angioedema and the threat of asphyxiation.
Angioedema
Refractory Abdominal Pain in a Patient with Chronic Lymphocytic Leukemia: Be Wary of Acquired Angioedema due to C1 Esterase Inhibitor Deficiency.
Angioedema
rhC1INH: a new drug for the treatment of attacks in hereditary angioedema caused by C1-inhibitor deficiency.
Angioedema
Safety and efficacy of C1 esterase inhibitor for acute attacks in children with hereditary angioedema.
Angioedema
The Genetics of Hereditary Angioedema: A Review.
Angioedema
The isolated angioedema of the bowel due to C1 esterase inhibitor deficiency: a case report and review of literature.
Angioedema
The late onset form of C1 esterase-inhibitor deficiency presenting as food allergy.
Angioedema
The Role of C1-Esterase Inhibitors in the Management of Vasogenic Edema in Glioblastoma.
Angioedema
The Use of Plasma-Derived Complement C1-Esterase Inhibitor Concentrate (Berinert®) in the Treatment of Angiotensin Converting Enzyme-Inhibitor Related Angioedema.
Angioedema
Treatment of Hereditary Angioedema.
Angioedema
Unmasking of acquired autoimmune C1-inhibitor deficiency by an angiotensin-converting enzyme inhibitor.
Angioedema
Unusual Case of a Massive Macroglossia Secondary to Myxedema: A Case Report and Literature Review.
Angioedema
Update on the acute treatment of hereditary angioedema.
Angioedema
Update on the Use of C1-Esterase Inhibitor Replacement Therapy in the Acute and Prophylactic Treatment of Hereditary Angioedema.
Angioedema
Urticaria and angioedema.
Angioedema
Urticaria and angioedema: diagnosis and evaluation.
Angioedema
[A patient with angioedema due to acquired C1 esterase inhibitor deficiency]
Angioedema
[Acquired angioneurotic edema caused by acquired deficiency of C1 esterase inhibitor disclosing lymphoproliferative syndrome. Apropos of a case, review of the literature]
Angioedema
[Acquired C1-esterase inhibitor deficiency with angioedema in lymphoplasmocytic lymphoma]
Angioedema
[Acquired C1 esterase inhibitor deficiency via bradykinin-mediated angioedema: Four cases].
Angioedema
[Anaesthesic management of vaginal delivery in a parturient with C1 esterase deficiency]
Angioedema
[Anesthesia and perioperative management in a patient with acquired angioedema].
Angioedema
[Angioedema caused by C1 esterase inhibitor deficiency]
Angioedema
[Angioedema caused by C1-esterase inhibitor deficiency or ACE inhibitors?]
Angioedema
[Angioedema: first manifestation of non-Hodgkin's lymphoma]
Angioedema
[Angioneurotic edema in hereditary alpha-1-antitrypsin deficiency]
Angioedema
[Angioneurotic orolingual edema associated with the use of rt-PA following a stroke.]
Angioedema
[C1-esterase inhibitor in ACE inhibitor-induced severe angioedema of the tongue]
Angioedema
[Correction of deficiency of C1 esterase inhibitor in angioneurotic edema with oxymetholone]
Angioedema
[Episodes of angioedema in children with C1 esterase inhibitor deficiency]
Angioedema
[Hereditary angioedema due to C1-esterase inhibitor deficiency?: novel approaches].
Angioedema
[Hereditary angioedema of delayed onset]
Angioedema
[Hereditary deficiency of C1-esterase inhibitor presenting with recurrent abdominal pain]
Angioedema
[Immunocytoma with acquired C1-esterase inhibitor deficiency and recurrent angioneurotic edema]
Angioedema
[Profhylaxis and treatment of hereditary and acquired angioedema at HUB; use of the C1-esterase inhibitor]
Angioedemas, Hereditary
A Case of Angioedema Due to Acquired C1 Esterase Inhibitor Deficiency Masquerading as Suspected Peritonitis: A Case Report.
Angioedemas, Hereditary
A case of hereditary angioedema in a 7-year-old korean girl.
Angioedemas, Hereditary
A case of hereditary angioedema who presented with difficulty in urination and globe.
Angioedemas, Hereditary
A Case of Type 2 Hereditary Angioedema With SERPING1 Mutation.
Angioedemas, Hereditary
A Decade of Change: Recent Developments in Pharmacotherapy of Hereditary Angioedema (HAE).
Angioedemas, Hereditary
A first of its kind quantitative functional C1-esterase inhibitor lateral flow assay for hereditary angioedema point-of-care diagnostic testing.
Angioedemas, Hereditary
A novel functional C1 inhibitor activity assay in dried blood spot for diagnosis of Hereditary angioedema.
Angioedemas, Hereditary
A novel series of arylsulfonylthiophene-2-carboxamidine inhibitors of the complement component C1s.
Angioedemas, Hereditary
A rare cause of recurrent priapism: hereditary angioedema.
Angioedemas, Hereditary
A recombinant C1 esterase inhibitor (Ruconest) for hereditary angioedema.
Angioedemas, Hereditary
A review of kallikrein inhibitor lanadelumab in hereditary angioedema.
Angioedemas, Hereditary
A review of the reported defects in the human C1 esterase inhibitor gene producing hereditary angioedema including four new mutations.
Angioedemas, Hereditary
A robust multiplexed assay to quantify C1-inhibitor, C1q, and C4 proteins for in vitro diagnosis of hereditary angioedema from dried blood spot.
Angioedemas, Hereditary
Acquired and hereditary forms of recurrent angioedema: Update of treatment.
Angioedemas, Hereditary
Acquired C1 esterase inhibitor deficiency and angioedema: a review.
Angioedemas, Hereditary
Acquired C1 esterase inhibitor deficiency as manifestation of T-cell lymphoproliferative disorder.
Angioedemas, Hereditary
Acquired C1 esterase inhibitor deficiency causing intestinal angioedema: CT appearance.
Angioedemas, Hereditary
Acquired C1 esterase inhibitor deficiency in a marginal zone lymphoma patient treated with rituximab.
Angioedemas, Hereditary
Acquired C1 esterase inhibitor deficiency in lymphomas: prevalence, symptoms, and response to treatment.
Angioedemas, Hereditary
Acquired C1 esterase inhibitor deficiency in two patients presenting with a lupus-like syndrome and anticardiolipin antibodies.
Angioedemas, Hereditary
Acquired C1 esterase inhibitor deficiency or serendipity? The chance finding of a paraprotein after an apparently low C1 esterase inhibitor concentration.
Angioedemas, Hereditary
Acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Acquired C1 Esterase Inhibitor Deficiency.
Angioedemas, Hereditary
Acquired C1 esterase inhibitor deficiency: An atypical first presentation intra-operatively.
Angioedemas, Hereditary
Acquired C1 inhibitor deficiency: postmortem diagnosis.
Angioedemas, Hereditary
Acquired complement C1 esterase inhibitor deficiency in a patient with a rare SERPING1 variant with unknown significance.
Angioedemas, Hereditary
Acute Genital Swelling Heralding C1 Esterase Inhibitor Deficiency in a Child.
Angioedemas, Hereditary
Acute pancreatitis due to hereditary angioedema.
Angioedemas, Hereditary
Acute upper airway angioedema secondary to acquired C1 esterase inhibitor deficiency: a case report.
Angioedemas, Hereditary
Acute upper airway obstruction from acquired angioedema.
Angioedemas, Hereditary
Administration of conestat alfa, human C1 esterase inhibitor and icatibant in the treatment of acute angioedema attacks in adults with hereditary angioedema due to C1 esterase inhibitor deficiency. Treatment comparison based on systematic review results.
Angioedemas, Hereditary
Advances in basic and clinical immunology in 2009.
Angioedemas, Hereditary
Allergic urticaria and hereditary angioedema. Independent association in the same patient.
Angioedemas, Hereditary
An adverse reaction to angiotensin-converting enzyme inhibitors in a patient with neglected C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
An association between C1 esterase inhibitor deficiency and lupus erythematosus: report of two cases and review of the literature.
Angioedemas, Hereditary
An evidence based therapeutic approach to hereditary and acquired angioedema.
Angioedemas, Hereditary
An investigational RNAi therapeutic targeting Factor XII (ALN-F12) for the treatment of hereditary angioedema.
Angioedemas, Hereditary
An update on the diagnosis and management of hereditary angioedema with abnormal c1 inhibitor.
Angioedemas, Hereditary
Anaesthesia Management of a Patient with Hereditary Angioedema with Prophylactic Administration of C1 Esterase Inhibitor: Case report and literature review.
Angioedemas, Hereditary
Anaesthetic Management of a Patient with Hereditary Angioedema.
Angioedemas, Hereditary
Angio-oedema--? acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Angioedema and acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Angioedema in a child with a liver transplant, intussusception, and normal c4 levels.
Angioedemas, Hereditary
Angioedema in a patient with c1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Angioedema in the emergency department: a presentation of lymphoma.
Angioedemas, Hereditary
Angioedema of the tongue due to acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Angioedema presenting in the retropharyngeal space in an adult.
Angioedemas, Hereditary
Angioedema secondary to angiotensin converting enzyme inhibitors is not due to C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Angioedema suppressed by a combination of anti-histamine and leukotriene modifier.
Angioedemas, Hereditary
Angioedema: frightening and frustrating.
Angioedemas, Hereditary
Angioedema: manifestations and management.
Angioedemas, Hereditary
Angiotensin-converting enzyme (ACE) inhibitors and angio-oedema.
Angioedemas, Hereditary
Angiotensin-converting enzyme inhibitors-induced angioedema treated by C1 esterase inhibitor concentrate (Berinert®): about one case and review of the therapeutic arsenal.
Angioedemas, Hereditary
Antiepileptic drug-induced lymphoproliferative disorder associated with acquired C1 esterase inhibitor deficiency and angioedema.
Angioedemas, Hereditary
Asphyxiation by laryngeal edema in patients with hereditary angioedema.
Angioedemas, Hereditary
Biochemical comparison of four commercially available C1 esterase inhibitor concentrates for treatment of hereditary angioedema.
Angioedemas, Hereditary
Biphenylsulfonyl-thiophene-carboxamidine inhibitors of the complement component C1s.
Angioedemas, Hereditary
Budgetary Impact of Medicinal Therapies for Rare Diseases in Bulgaria.
Angioedemas, Hereditary
C1 esterase inhibitor activity is reduced in the acute phase following burn injury: a prospective observational study.
Angioedemas, Hereditary
C1 esterase inhibitor concentrate in 1085 Hereditary Angioedema attacks--final results of the I.M.P.A.C.T.2 study.
Angioedemas, Hereditary
C1 esterase inhibitor deficiency as a cause of abdominal pain.
Angioedemas, Hereditary
C1 esterase inhibitor deficiency in X-linked hypogammaglobulinaemia: an anomaly fostering anaphylactoid reactions following intramuscular gammaglobulin administration.
Angioedemas, Hereditary
C1 esterase inhibitor deficiency, airway compromise, and anesthesia.
Angioedemas, Hereditary
C1 esterase inhibitor deficiency: three presentations.
Angioedemas, Hereditary
C1 esterase inhibitor transfusions in patients with hereditary angioedema.
Angioedemas, Hereditary
C1-esterase inhibitor for short-term prophylaxis in a patient with hereditary angioedema with normal C1 inhibitor function.
Angioedemas, Hereditary
C1-esterase inhibitor transfusions in patients with hereditary angioedema.
Angioedemas, Hereditary
C1-esterase inhibitor treatment: preclinical safety aspects on the potential prothrombotic risk.
Angioedemas, Hereditary
C1-Esterase inhibitor: an anti-inflammatory agent and its potential use in the treatment of diseases other than hereditary angioedema.
Angioedemas, Hereditary
Calcium channel blocker-associated small bowel angioedema.
Angioedemas, Hereditary
Capillary leak syndrome and disseminated intravascular coagulation after kidney transplantation in a patient with hereditary angioedema - A case report.
Angioedemas, Hereditary
Chapter 22: Hereditary and acquired angioedema.
Angioedemas, Hereditary
Chapter 25: Idiopathic anaphylaxis.
Angioedemas, Hereditary
Characteristics of patients with C1 esterase inhibitor deficiency: a single center study.
Angioedemas, Hereditary
Characterization of acute hereditary angioedema attacks during pregnancy and breast-feeding and their treatment with C1 inhibitor concentrate.
Angioedemas, Hereditary
Cinryze as the first approved C1 inhibitor in the USA for the treatment of hereditary angioedema: approval, efficacy and safety.
Angioedemas, Hereditary
Cinryze, a Human Plasma-Derived C1 Esterase Inhibitor for Prophylaxis Of Hereditary Angioedema.
Angioedemas, Hereditary
Clinical Pattern and Acute and Long-term Management of Hereditary Angioedema Due to C1-Esterase Inhibitor Deficiency.
Angioedemas, Hereditary
Clinical review of hereditary angioedema: diagnosis and management.
Angioedemas, Hereditary
Clinical studies of sudden upper airway obstruction in patients with hereditary angioedema due to C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Co-occurrence between C1 esterase inhibitor deficiency and autoimmune disease: a systematic literature review.
Angioedemas, Hereditary
Complement activation during bypass in acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Complement analysis in adult patients with a history of bacteremic pneumococcal infections or recurrent pneumonia.
Angioedemas, Hereditary
Complement component analysis in angiodema. Diagnostic value.
Angioedemas, Hereditary
Complement deficiency and disease: an update.
Angioedemas, Hereditary
Complement Inhibition for Prevention and Treatment of Antibody-Mediated Rejection in Renal Allograft Recipients.
Angioedemas, Hereditary
Conestat alfa (ruconest): first recombinant c1 esterase inhibitor for the treatment of acute attacks in patients with hereditary angioedema.
Angioedemas, Hereditary
Contraindications to the use of ace inhibitors in patients with C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Correction of recurrent angioedema related to C1 esterase inhibitor deficiency as a secondary event following nonmyeloablative allogeneic stem cell transplantation in a patient with myelofibrosis.
Angioedemas, Hereditary
Cost-utility analysis of Ruconest(®) (conestat alfa) compared to Berinert(®) P (human C1 esterase inhibitor) in the treatment of acute, life-threatening angioedema attacks in patients with hereditary angioedema.
Angioedemas, Hereditary
CT Findings of Acute Small-Bowel Entities.
Angioedemas, Hereditary
Current and Prospective Targets of Pharmacologic Treatment of Hereditary Angioedema Types 1 and 2.
Angioedemas, Hereditary
Current management options for hereditary angioedema.
Angioedemas, Hereditary
Current options for prophylactic treatment of hereditary angioedema in the United States: patient-based considerations.
Angioedemas, Hereditary
Danazol and C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Death due to obstruction of the upper airways caused by edema of the laryngeal mucosa in the course of hereditary angioedema.
Angioedemas, Hereditary
Diagnosis and management of angioedema with abdominal involvement: a gastroenterology perspective.
Angioedemas, Hereditary
Diminished capacity of opsonization and immune complex solubilization, and detection of anti-C1q antibodies in sera from patients with hereditary angioedema.
Angioedemas, Hereditary
Discrepancies between guidelines and international practice in treatment of hereditary angioedema.
Angioedemas, Hereditary
Does heparin prophylaxis prevent exacerbations of hereditary angioedema?
Angioedemas, Hereditary
DX-88 and HAE: a developmental perspective.
Angioedemas, Hereditary
Ecallantide for the treatment of hereditary angiodema in adults.
Angioedemas, Hereditary
Ecallantide for treatment of acute attacks of acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Effect of C1 esterase inhibitor in hereditary angioedema treatment.
Angioedemas, Hereditary
Effect of dehydroepiandrosterone on hereditary angioedema.
Angioedemas, Hereditary
Effect of time to treatment on response to C1 esterase inhibitor concentrate for hereditary angioedema attacks.
Angioedemas, Hereditary
Effects of a plasma-derived C1 esterase inhibitor on hemostatic activation, clot formation, and thrombin generation.
Angioedemas, Hereditary
Efficacy Assessments in Randomized Controlled Studies of Acute Therapy for Hereditary Angioedema.
Angioedemas, Hereditary
Efficacy of C1 esterase inhibitor concentrate in treatment of cutaneous attacks of hereditary angioedema.
Angioedemas, Hereditary
Efficacy of Different Medical Therapies for the Treatment of Acute Laryngeal Attacks of Hereditary Angioedema due to C1-esterase Inhibitor Deficiency.
Angioedemas, Hereditary
Efficacy of human C1 esterase inhibitor concentrate compared with placebo in acute hereditary angioedema attacks.
Angioedemas, Hereditary
Efficacy of recombinant human C1 esterase inhibitor across anatomic locations in acute hereditary angioedema attacks.
Angioedemas, Hereditary
Efficacy of recombinant human C1 esterase inhibitor for the treatment of severe hereditary angioedema attacks.
Angioedemas, Hereditary
Elevated D-dimers in attacks of hereditary angioedema are not associated with increased thrombotic risk.
Angioedemas, Hereditary
Escalating doses of C1 esterase inhibitor (CINRYZE) for prophylaxis in patients with hereditary angioedema.
Angioedemas, Hereditary
Exacerbation of a lupus-erythematosus-like syndrome during treatment of non-C1-esterase-inhibitor-dependent angioedema with danazol.
Angioedemas, Hereditary
Exposure-Response Model of Subcutaneous C1-Inhibitor Concentrate to Estimate the Risk of Attacks in Patients With Hereditary Angioedema.
Angioedemas, Hereditary
Factor XII-Driven Inflammatory Reactions with Implications for Anaphylaxis.
Angioedemas, Hereditary
Falsely normal C4 in a case of acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Feasibility of home infusion and self-administration of nanofiltered C1 esterase inhibitor for routine prophylaxis in patients with hereditary angioedema and characterization of a training and support program.
Angioedemas, Hereditary
Fresh frozen plasma for on-demand hereditary angioedema treatment in South Africa and Iran.
Angioedemas, Hereditary
Gene Therapy for C1 Esterase Inhibitor Deficiency in a Murine Model of Hereditary Angioedema.
Angioedemas, Hereditary
General and subarachnoid anaesthesia in a patient with acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Genetically determined heterogeneity of the C1 esterase inhibitor in patients with hereditary angioneurotic edema.
Angioedemas, Hereditary
Glomerulonephritis and hereditary angioedema: report of 2 cases.
Angioedemas, Hereditary
Guillain-Barré syndrome following danazol and corticosteroid therapy for hereditary angioedema.
Angioedemas, Hereditary
HAEdb: a novel interactive, locus-specific mutation database for the C1 inhibitor gene.
Angioedemas, Hereditary
Haegarda--a subcutaneous C1 esterase inhibitor for prevention of hereditary angioedema.
Angioedemas, Hereditary
Hereditary and acquired angioedema.
Angioedemas, Hereditary
Hereditary and acquired angioedema: problems and progress: proceedings of the third C1 esterase inhibitor deficiency workshop and beyond.
Angioedemas, Hereditary
Hereditary and acquired complement component 1 esterase inhibitor deficiency: a review for the hematologist.
Angioedemas, Hereditary
Hereditary angioedema and pregnancy.
Angioedemas, Hereditary
Hereditary angioedema and pregnancy: a successful outcome using C1 esterase inhibitor concentrate.
Angioedemas, Hereditary
Hereditary angioedema and pregnancy: successful management of recurrent and frequent attacks of angioedema with C1-inhibitor concentrate, danazol and tranexamic acid - a case report.
Angioedemas, Hereditary
Hereditary angioedema associated with heterozygous factor V Leiden mutation in a patient with Purpura fulminans.
Angioedemas, Hereditary
Hereditary Angioedema Attack in Utero and Treatment of the Mother and Fetus.
Angioedemas, Hereditary
Hereditary angioedema C1-esterase inhibitor replacement therapy and coexisting autoimmune disorders: findings from a claims database.
Angioedemas, Hereditary
Hereditary angioedema caused by c1-esterase inhibitor deficiency: a literature-based analysis and clinical commentary on prophylaxis treatment strategies.
Angioedemas, Hereditary
Hereditary angioedema due to deficit of C1 esterase inhibitor.
Angioedemas, Hereditary
Hereditary angioedema managed with low-dose danazol and c1 esterase inhibitor concentrate: a case report.
Angioedemas, Hereditary
Hereditary angioedema presenting as epiglottitis.
Angioedemas, Hereditary
Hereditary angioedema therapy: kallikrein inhibition and bradykinin receptor antagonism.
Angioedemas, Hereditary
Hereditary angioedema type 2 presented as an orbital complication of acute rhinosinusitis.
Angioedemas, Hereditary
Hereditary angioedema type II--a study of two families.
Angioedemas, Hereditary
Hereditary angioedema with C1 inhibitor (C1-INH) deficit: the strength of recognition (51 cases).
Angioedemas, Hereditary
Hereditary angioedema with recurrent abdominal pain.
Angioedemas, Hereditary
Hereditary angioedema.
Angioedemas, Hereditary
Hereditary angioedema. Diagnosis in an asymptomatic elderly woman.
Angioedemas, Hereditary
Hereditary angioedema. Report of a large kindred with a rare genetic variant of C1-esterase inhibitor.
Angioedemas, Hereditary
Hereditary angioedema: a clinical review for the otolaryngologist.
Angioedemas, Hereditary
Hereditary angioedema: a family study.
Angioedemas, Hereditary
HEREDITARY ANGIOEDEMA: A Literature Review and National Management Guidelines.
Angioedemas, Hereditary
Hereditary angioedema: a Taiwanese family with a novel gene mutation.
Angioedemas, Hereditary
Hereditary angioedema: an update on causes, manifestations and treatment.
Angioedemas, Hereditary
Hereditary angioedema: imaging manifestations and clinical management.
Angioedemas, Hereditary
Hereditary angioedema: new hopes for an orphan disease.
Angioedemas, Hereditary
Hereditary angioedema: not an allergy.
Angioedemas, Hereditary
Hereditary angioedema: quality of life in Brazilian patients.
Angioedemas, Hereditary
Hereditary angioedema: report of a case.
Angioedemas, Hereditary
Hereditary angioedema: report of a large kindred with a rare genetic variant of C1-esterase inhibitor.
Angioedemas, Hereditary
Hereditary angioedema: therapeutic effect of danazol on C4 and C1 esterase inhibitors.
Angioedemas, Hereditary
Hereditary angioneurotic edema (HANE): Lack of close linkage between HLA haplotypes and C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Hereditary angioneurotic edema and functional C1 esterase inhibitor.
Angioedemas, Hereditary
Hereditary angioneurotic edema of the larynx.
Angioedemas, Hereditary
Hereditary angioneurotic edema treated by partial uvulectomy.
Angioedemas, Hereditary
Hereditary angioneurotic oedema: a neglected diagnosis.
Angioedemas, Hereditary
High amounts of beta-endorphin in peripheral blood mononuclear cells from HANE patients.
Angioedemas, Hereditary
Home therapy with intravenous human C1-inhibitor in children and adolescents with hereditary angioedema.
Angioedemas, Hereditary
Hormonally exacerbated hereditary angioedema.
Angioedemas, Hereditary
Human C1-esterase inhibitor concentrate (Berinert).
Angioedemas, Hereditary
Human parvovirus infection: rheumatic manifestations, angioedema, C1 esterase inhibitor deficiency, ANA positivity, and possible onset of systemic lupus erythematosus.
Angioedemas, Hereditary
Icatibant. Attacks of hereditary angioedema: continue to use C1 esterase inhibitor.
Angioedemas, Hereditary
Idiopathic anaphylaxis.
Angioedemas, Hereditary
In Vitro Modeling of Bradykinin-Mediated Angioedema States.
Angioedemas, Hereditary
Increased fibrinolysis-induced bradykinin formation in hereditary angioedema confirmed using stored plasma and biotechnological inhibitors.
Angioedemas, Hereditary
Indirect Comparison of Lanadelumab and Intravenous C1-INH Using Data from the HELP and CHANGE Studies: Bayesian and Frequentist Analyses.
Angioedemas, Hereditary
Inherited disorders of complement.
Angioedemas, Hereditary
Inhibition of the serine proteases of the complement system.
Angioedemas, Hereditary
Interactive Web-Based Resource for Annotation of Genetic Variants Causing Hereditary Angioedema (HADA): Database Development, Implementation, and Validation.
Angioedemas, Hereditary
Intestinal angioedema caused by an acquired C1 esterase inhibitor deficiency associated with underlying splenic marginal zone lymphoma.
Angioedemas, Hereditary
Is there a need for clinical guidelines in the United States for the diagnosis of hereditary angioedema and the screening of family members of affected patients?
Angioedemas, Hereditary
Isolated angioedema of the bowel due to C1 esterase inhibitor deficiency: a case report and review of literature.
Angioedemas, Hereditary
Kallikrein-kinin system and fibrinolysis in hereditary angioedema due to factor XII gene mutation Thr309Lys.
Angioedemas, Hereditary
Laboratory testing for C1 inhibitor deficiency: a comparison of two approaches to C1 inhibitor function.
Angioedemas, Hereditary
Lanadelumab for the prevention of attacks in hereditary angioedema.
Angioedemas, Hereditary
Lanadelumab for the Prophylactic Treatment of Hereditary Angioedema with C1 Inhibitor Deficiency: A Review of Preclinical and Phase I Studies.
Angioedemas, Hereditary
Long-standing angioedema with C1 esterase inhibitor deficiency associated with occult lymphoma.
Angioedemas, Hereditary
Long-term health-related quality of life in patients treated with subcutaneous C1-inhibitor replacement therapy for the prevention of hereditary angioedema attacks: findings from the COMPACT open-label extension study.
Angioedemas, Hereditary
Long-term outcomes with subcutaneous C1-inhibitor replacement therapy for prevention of hereditary angioedema attacks.
Angioedemas, Hereditary
Long-Term Prophylaxis of Hereditary Angioedema with a Pasteurized C1 Inhibitor Concentrate.
Angioedemas, Hereditary
Low molecular weight IgM in B cell lymphoproliferative disorders.
Angioedemas, Hereditary
Lupus anticoagulant and thrombosis in splenic marginal zone lymphoma.
Angioedemas, Hereditary
Lupus enteritis as the only active manifestation of systemic lupus erythematosus: A case report.
Angioedemas, Hereditary
Lymphocytic lymphoma and acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Mast cells increase vascular permeability by heparin-initiated bradykinin formation in vivo.
Angioedemas, Hereditary
Model-Based Evaluation of Similarity in Pharmacokinetics of Two Formulations of the Blood-Derived Plasma Product C1 Esterase Inhibitor.
Angioedemas, Hereditary
Modern preoperative and intraoperative management of hereditary angioedema.
Angioedemas, Hereditary
Modification of peripheral blood T-lymphocyte surface receptors and Langerhans cell numbers in hereditary angioedema.
Angioedemas, Hereditary
Molecular diagnosis and management of hereditary angioedema in a Greek family.
Angioedemas, Hereditary
Monoclonal gammopathy in association with allergic disorders of the skin and respiratory tract.
Angioedemas, Hereditary
Mutation screening of the C1 inhibitor gene among Hungarian patients with hereditary angioedema.
Angioedemas, Hereditary
Nanofiltered C1 esterase inhibitor (human) for hereditary angioedema attacks in pregnant women.
Angioedemas, Hereditary
Nanofiltered C1 esterase inhibitor (human) for the treatment of acute attacks of hereditary angioedema: an open-label trial.
Angioedemas, Hereditary
Nanofiltered C1 esterase inhibitor for treatment of laryngeal attacks in patients with hereditary angioedema.
Angioedemas, Hereditary
Nanofiltered C1-Esterase Inhibitor for the Acute Management and Prevention of Hereditary Angioedema Attacks due to C1-Inhibitor Deficiency in Children.
Angioedemas, Hereditary
Nephelometric and immunodiffusion assays for the fourth component of complement in acquired C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
New insights into hereditary angio-oedema: Molecular diagnosis and therapy.
Angioedemas, Hereditary
New mutations in C1 esterase inhibitor (SERPING1) in a German family with hereditary angioedema.
Angioedemas, Hereditary
New-variant hereditary angioedema in three brothers with normal C1 esterase inhibitor level and function.
Angioedemas, Hereditary
Novel Use of Fresh Frozen Plasma in Treating Hereditary Angioedema: A Success Story From Pakistan.
Angioedemas, Hereditary
Off-pump coronary artery bypass surgery in a patient with C1 esterase inhibitor deficiency.
Angioedemas, Hereditary
Ongoing contact activation in patients with hereditary angioedema.
Angioedemas, Hereditary
Optimizing hereditary angioedema management through tailored treatment approaches.
Angioedemas, Hereditary
Oral Plasma Kallikrein Inhibitor for Prophylaxis in Hereditary Angioedema.
Angioedemas, Hereditary
Orthodontic treatment for a patient with hereditary angiodema: a case report.
Angioedemas, Hereditary
Pasteurized and nanofiltered, plasma-derived C1 esterase inhibitor concentrate for the treatment of hereditary angioedema.
Angioedemas, Hereditary
Peptide inhibitor of complement c1, a novel suppressor of classical pathway activation: mechanistic studies and clinical potential.
Angioedemas, Hereditary
Peri-operative management of a patient with hereditary angioedema undergoing laparoscopic cholecystectomy.
Angioedemas, Hereditary
Perioperative course in patients with hereditary or acquired angioedema.
Angioedemas, Hereditary
Perioperative management for patients with hereditary angioedema.
Angioedemas, Hereditary
Perioperative management of a patient with hereditary angioedema during off-pump coronary artery bypass graft surgery.
Angioedemas, Hereditary
Perioperative Management of Patients With Hereditary Angioedema With Special Considerations for Cardiopulmonary Bypass.
Angioedemas, Hereditary
Perioperative management of tooth extractions for a patient with hereditary angioedema.
Angioedemas, Hereditary
Pharmaceutical approval update.
Angioedemas, Hereditary
Pharmacokinetics of plasma-derived C1-esterase inhibitor after subcutaneous versus intravenous administration in subjects with mild or moderate hereditary angioedema: the PASSION study.
Angioedemas, Hereditary
Plasma bradykinin in angio-oedema.
Angioedemas, Hereditary
Plasmin is a natural trigger for bradykinin production in patients with hereditary angioedema with factor XII mutations.
Angioedemas, Hereditary
Population pharmacokinetics of plasma-derived C1 esterase inhibitor concentrate used to treat acute hereditary angioedema attacks.
Angioedemas, Hereditary
Population pharmacokinetics of recombinant human C1 esterase inhibitor in children with hereditary angioedema.
Angioedemas, Hereditary
Population pharmacokinetics of subcutaneous C1-inhibitor for prevention of attacks in patients with hereditary angioedema.
Angioedemas, Hereditary
Possible disease-modifying factors: the mannan-binding lectin pathway and infections in hereditary angioedema of children and adults.
Angioedemas, Hereditary
Practical approach to self-administration of intravenous C1-INH concentrate: a nursing perspective.
Angioedemas, Hereditary
Practicalities of a reduced volume formulation of a C1-INH concentrate for the treatment of hereditary angioedema: real-life experience.
Angioedemas, Hereditary
Pregnancy and C1 esterase inhibitor deficiency: a successful outcome.
Angioedemas, Hereditary
Pregnancy-Induced Exacerbation of Hereditary Angioedema in a Multiparous Caucasian Female.
Angioedemas, Hereditary
Preprocedural administration of nanofiltered C1 esterase inhibitor to prevent hereditary angioedema attacks.
Angioedemas, Hereditary
Prevalence of hereditary angioedema in untested first-degree blood relatives of known subjects with hereditary angioedema.
Angioedemas, Hereditary
Prognostic factors in outcome of angioedema in the emergency department.
Angioedemas, Hereditary
Progress in the emergency management of hereditary angioedema: focus on new treatment options in the United States.
Angioedemas, Hereditary
Prospective study of C1 esterase inhibitor in the treatment of successive acute abdominal and facial hereditary angioedema attacks.
Angioedemas, Hereditary
Prospective study of rapid relief provided by c1 esterase inhibitor in emergency treatment of acute laryngeal attacks in hereditary angioedema.
Angioedemas, Hereditary
Randomized Trial of the Efficacy and Safety of Berotralstat (BCX7353) as an Oral Prophylactic Therapy for Hereditary Angioedema: Results of APeX-2 Through 48 Weeks (Part 2).
Angioedemas, Hereditary
Recent developments in the treatment of acute abdominal and facial attacks of hereditary angioedema: focus on human C1 esterase inhibitor.
Angioedemas, Hereditary
Recognition, Evaluation, and Management of Pediatric Hereditary Angioedema.
Angioedemas, Hereditary
Recombinant human C1 esterase inhibitor (Conestat alfa) for prophylaxis to prevent attacks in adult and adolescent patients with hereditary angioedema.
Angioedemas, Hereditary
Recombinant human C1 esterase inhibitor as short-term prophylaxis in patients with hereditary angioedema.
Angioedemas, Hereditary
Recombinant human C1 esterase inhibitor for acute hereditary angioedema attacks with upper airway involvement.
Angioedemas, Hereditary
Recombinant human C1 esterase inhibitor for hereditary angioedema attacks: A European registry.
Angioedemas, Hereditary
Recombinant human C1 esterase inhibitor for the treatment of hereditary angioedema due to C1 inhibitor deficiency (C1-INH-HAE).
Angioedemas, Hereditary
Recombinant human C1 esterase inhibitor in the management of hereditary angioedema.
Angioedemas, Hereditary
Recombinant human C1 esterase inhibitor treatment for hereditary angioedema attacks in children.
Angioedemas, Hereditary
Recombinant human C1-esterase inhibitor relieves symptoms of hereditary angioedema attacks: phase 3, randomized, placebo-controlled trial.
Angioedemas, Hereditary
Recombinant Human C1-Esterase Inhibitor to Treat Acute Hereditary Angioedema Attacks in Adolescents.
Angioedemas, Hereditary
Recombinant Human-C1 Inhibitor is Effective and Safe for Repeat Hereditary Angioedema Attacks.
Angioedemas, Hereditary
Recombinant replacement therapy for hereditary angioedema due to C1 inhibitor deficiency.
Angioedemas, Hereditary
Recurrent angioedema and the threat of asphyxiation.
Angioedemas, Hereditary
Recurrent angioedema: Experience at a tertiary care urban medical center.
Angioedemas, Hereditary
Recurrent angioedema: familial and oestrogen-induced.
Angioedemas, Hereditary
Refractory Abdominal Pain in a Patient with Chronic Lymphocytic Leukemia: Be Wary of Acquired Angioedema due to C1 Esterase Inhibitor Deficiency.
Angioedemas, Hereditary
Repeated attacks of type III hereditary angioedema with factor XII mutation during pregnancy.
Angioedemas, Hereditary
Replacement therapy with C1 esterase inhibitors for hereditary angioedema.
Angioedemas, Hereditary
Safety and efficacy of C1 esterase inhibitor for acute attacks in children with hereditary angioedema.
Angioedemas, Hereditary
Safety of c1-esterase inhibitor in acute and prophylactic therapy of hereditary angioedema: findings from the ongoing international berinert patient registry.
Angioedemas, Hereditary
Safety of recombinant human C1 esterase inhibitor for hereditary angioedema attacks during pregnancy.
Angioedemas, Hereditary
Self-administered C1 esterase inhibitor concentrates for the management of hereditary angioedema: usability and patient acceptance.
Angioedemas, Hereditary
Self-administration of intravenous C1 esterase inhibitor (Berinertâ) in patients with Hereditary Angioedema decreases number of days spent in an emergency room.
Angioedemas, Hereditary
Self-administration of intravenous C1 esterase inhibitor in hereditary angioedema.
Angioedemas, Hereditary
Social costs of icatibant self-administration vs. health professional-administration in the treatment of hereditary angioedema in Spain.
Angioedemas, Hereditary
Some properties of proteolysis by polymorphonuclear leukocyte-granule extracts.
Angioedemas, Hereditary
Sonographic appearances of the abdominal manifestations of hereditary angioedema.
Angioedemas, Hereditary
Spontaneous regression of acquired C1 esterase inhibitor deficiency associated with splenic marginal zone lymphoma presenting with recurrent angio-oedema.
Angioedemas, Hereditary
Study of angiopoietin and plasminogen genes in hereditary angioedema.
Angioedemas, Hereditary
Subcutaneous C1 inhibitor for prevention of attacks of hereditary angioedema: additional outcomes and subgroup analysis of a placebo-controlled randomized study.
Angioedemas, Hereditary
Subcutaneous C1-esterase inhibitor to prevent hereditary angioedema attacks: Safety findings from the COMPACT trial.
Angioedemas, Hereditary
Successful anesthetic management during abdominal wall-lifting laparoscopic cholecystectomy in a patient with hereditary angioedema.
Angioedemas, Hereditary
Successful C1 inhibitor short-term prophylaxis during redo mitral valve replacement in a patient with hereditary angioedema.
Angioedemas, Hereditary
Successful extubation with use of C1 esterase inhibitor concentrate in a patient with hereditary angioedema.
Angioedemas, Hereditary
Successful Long-Term Prophylactic Treatment With Subcutaneous C1 Esterase Inhibitor in a Patient With Hereditary Angioedema.
Angioedemas, Hereditary
Successful long-term treatment with the bradykinin B2 receptor antagonist icatibant in a patient with hereditary angioedema.
Angioedemas, Hereditary
Successful management of hereditary angioedema during tonsillectomy: a case report.
Angioedemas, Hereditary
Successful perinatal management of hereditary angioedema with normal C1 esterase inhibitor and factor XII mutation using C1 esterase inhibitor therapy.
Angioedemas, Hereditary
Successful perioperative management of a patient with C1 esterase inhibitor deficiency with a novel bradykinin receptor B2 antagonist.
Angioedemas, Hereditary
Successful perioperative management of three patients with hereditary angioedema without C1 esterase inhibitor therapy: A developing country perspective.
Angioedemas, Hereditary
Successful resolution of bowel obstruction in a patient with hereditary angioedema.
Angioedemas, Hereditary
Successful treatment of acute hereditary angioedema attacks with self-administered icatibant in patients with venous access problems.
Angioedemas, Hereditary
Successful use of C1 esterase inhibitor protein in a patient with hereditary angioneurotic edema requiring coronary artery bypass surgery.
Angioedemas, Hereditary
Successful use of daily intravenous infusion of C1 esterase inhibitor concentrate in the treatment of a hereditary angioedema patient with ascites, hypovolemic shock, sepsis, renal and respiratory failure.
Angioedemas, Hereditary
Supplementation of C1-esterase inhibitor concentrates for a patient suffering from hereditary angioedema undergoing complex open-heart surgery.
Angioedemas, Hereditary
Sustained response of recombinant human C1 esterase inhibitor for acute treatment of hereditary angioedema attacks.
Angioedemas, Hereditary
The C1 esterase inhibitor and hereditary angioedema.
Angioedemas, Hereditary
The complex alteration in the network of IL-17-type cytokines in patients with hereditary angioedema.
Angioedemas, Hereditary
The Effect of Weight on the Efficacy and Safety of C1 Esterase Inhibitor Concentrate for the Treatment of Acute Hereditary Angioedema.
Angioedemas, Hereditary
The Effectiveness and Value of Lanadelumab and C1 Esterase Inhibitors for Prophylaxis of Hereditary Angioedema Attacks.
Angioedemas, Hereditary
The isolated angioedema of the bowel due to C1 esterase inhibitor deficiency: a case report and review of literature.
Angioedemas, Hereditary
The spectrum and treatment of angioedema.
Angioedemas, Hereditary
The thrombogenicity of C1 esterase inhibitor (human): review of the evidence.
Angioedemas, Hereditary
The value of C1 esterase inhibitor in patients with aspirin-sensitive urticaria.
Angioedemas, Hereditary
Therapeutic inhibition of the complement system. Y2K update.
Angioedemas, Hereditary
Thrombotic Events Associated with C1 Esterase Inhibitor Products in Patients with Hereditary Angioedema: Investigation from the United States Food and Drug Administration Adverse Event Reporting System Database.
Angioedemas, Hereditary
Thrombotic events associated with C1 esterase inhibitor products in patients with hereditary angioedema: investigation from the United States Food and Drug Administration adverse event reporting system database.
Angioedemas, Hereditary
Tissue Plasminogen Activator-Induced Angioedema Involving a Posterior Cerebral Artery Infarct: A Case Presentation.
Angioedemas, Hereditary
Training hereditary angioedema patients to self-administer intravenous C1 esterase inhibitor concentrate.
Angioedemas, Hereditary
Treatment for hereditary angioedema with normal C1-INH and specific mutations in the F12 gene (HAE-FXII).
Angioedemas, Hereditary
Treatment of hereditary angioedema with nanofiltered C1-esterase inhibitor concentrate (Cetor®): Multi-center phase II and III studies to assess pharmacokinetics, clinical efficacy and safety.
Angioedemas, Hereditary
Treatment of hereditary angioedema with plasma-derived C1 inhibitor.
Angioedemas, Hereditary
Treatment of Hereditary Angioedema.
Angioedemas, Hereditary
Treatment of Hereditary Angioedema: items that need to be addressed in practice parameter.
Angioedemas, Hereditary
Treatment response after repeated administration of C1 esterase inhibitor for successive acute hereditary angioedema attacks.
Angioedemas, Hereditary
Treatment with C1-esterase inhibitor concentrate in type I or II hereditary angioedema: a systematic literature review.
Angioedemas, Hereditary
Type I hereditary angioedema in Taiwan -- clinical, biological features and genetic study.
Angioedemas, Hereditary
Unusual manifestations of hereditary angioedema.
Angioedemas, Hereditary
Update on preventive therapy (prophylaxis) of hereditary angioedema.
Angioedemas, Hereditary
Update on the acute treatment of hereditary angioedema.
Angioedemas, Hereditary
Update on the Use of C1-Esterase Inhibitor Replacement Therapy in the Acute and Prophylactic Treatment of Hereditary Angioedema.
Angioedemas, Hereditary
Urticaria and angioedema.
Angioedemas, Hereditary
Urticaria and angioedema: diagnosis and evaluation.
Angioedemas, Hereditary
Urticarial vasculitis and asymptomatic acquired C1 esterase inhibitor deficiency revealing an angioimmunoblastic T cell lymphoma.
Angioedemas, Hereditary
Urticarial vasculitis, IgA deficiency and C1 esterase inhibitor deficiency in the presence of an IgG monoclonal gammopathy--a case report.
Angioedemas, Hereditary
Use of purified C1 esterase inhibitor in patients with hereditary angioedema.
Angioedemas, Hereditary
Usefulness of C1 esterase inhibitor protein concentrate in the management of hereditary angioedema of oropharyngeal tissue.
Angioedemas, Hereditary
When is prophylaxis for hereditary angioedema necessary?
Angioedemas, Hereditary
[67-year-old patient with speech disorder and dysphagia]
Angioedemas, Hereditary
[A case of lung cancer with hereditary angioedema treated effectively by chemo-radiotherapy with C1 esterase inhibitor concentrate and danazol]
Angioedemas, Hereditary
[A patient with angioedema due to acquired C1 esterase inhibitor deficiency]
Angioedemas, Hereditary
[Acquired C1 esterase inhibitor deficiency and lymphoproliferative syndromes]
Angioedemas, Hereditary
[Acquired C1 esterase inhibitor deficiency, Gougerot-Sjögren syndrome and B lymphoma]
Angioedemas, Hereditary
[Angioedema caused by C1 esterase inhibitor deficiency]
Angioedemas, Hereditary
[Attacks of abdominal pain in a young Turkish woman with C1 esterase inhibitor deficiency]
Angioedemas, Hereditary
[Behavior of esterase inhibitor C1 in patients with urticaria due to aspirin hypersensitivity]
Angioedemas, Hereditary
[C1 esterase inhibitor deficiency as a rare cause of recurrent acute abdominal pain]
Angioedemas, Hereditary
[Caesarean section in a parturient with C1 esterase inhibitor deficiency (angioneurotic oedema)]
Angioedemas, Hereditary
[Clinical facets of hereditary angioedema among Swiss patients].
Angioedemas, Hereditary
[Croup syndrome]
Angioedemas, Hereditary
[Efficacy of short-term danazol treatment in hereditary angioneurotic edema patients undergoing maxillofacial and dental surgical procedures]
Angioedemas, Hereditary
[Episodes of angioedema in children with C1 esterase inhibitor deficiency]
Angioedemas, Hereditary
[Hereditary angioedema by defict of C1 esterase. Our experience in 8 cases]
Angioedemas, Hereditary
[Hereditary angioedema caused by a deficiency of C1 esterase inhibitor. A sporadic case of late appearance]
Angioedemas, Hereditary
[Hereditary angioedema due to C1-esterase inhibitor deficiency]
Angioedemas, Hereditary
[Hereditary angioedema in Costa Rica].
Angioedemas, Hereditary
[Hereditary angioedema in the German-speaking region]
Angioedemas, Hereditary
[Hereditary angioedema of delayed onset]
Angioedemas, Hereditary
[Hereditary angioedema, a rare cause of recurrent abdominal pains. A report of 2 clinical cases and comments of a general nature]
Angioedemas, Hereditary
[Hereditary angioedema--neglected diagnosis].
Angioedemas, Hereditary
[Hereditary angioedema. A report of a case and literature review]
Angioedemas, Hereditary
[Hereditary angioedema. Description of a pediatric case]
Angioedemas, Hereditary
[Hereditary angioedema. Effect of danazol on C4 and functional C1INH]
Angioedemas, Hereditary
[Hereditary angioneurotic edema in children]
Angioedemas, Hereditary
[Hereditary angioneurotic edema: a molecular disease caused by a defect in the O-glycosylation of C1 esterase inhibitor (C1-INH)]
Angioedemas, Hereditary
[Hereditary C1 esterase inhibitor deficiency type I. Divergence of clinical symptoms and laboratory chemical findings]
Angioedemas, Hereditary
[Hereditary deficiency of C1-esterase inhibitor presenting with recurrent abdominal pain]
Angioedemas, Hereditary
[Mixed nodular lymphoma in association with a C1 esterase inhibitor deficiency (author's transl)]
Angioedemas, Hereditary
[New possibilities of treating acute angioedema caused by C1-inhibitor deficiency]
Angioedemas, Hereditary
[Recurrent attacks of angioedema ascribed to the use of estrogen preparations and a pregnancy (hereditary angioedema type 3)]
Angioedemas, Hereditary
[Simultaneous occurrence of hereditary angioneurotic edema and Crohn disease]
Angioedemas, Hereditary
[Sonography in hereditary angioedema: typical findings demonstrated by the example of 3 cases]
Angioedemas, Hereditary
[Study by means of enzymatic and immunochemical determination of Cl esterase inhibitor in 59 patients with hereditary angioneurotic edema]
Angioedemas, Hereditary
[Therapeutic approach of hereditary angioedema]
Arthritis
Key Components of the Complement Lectin Pathway Are Not Only Required for the Development of Inflammatory Arthritis but Also Regulate the Transcription of Factor D.
Arthritis, Rheumatoid
Association of MASP-2 Levels and MASP2 Gene Polymorphisms with Rheumatoid Arthritis in Patients and Their Relatives.
Arthritis, Rheumatoid
Complement C1s activation in degenerating articular cartilage of rheumatoid arthritis patients: immunohistochemical studies with an active form specific antibody.
Arthritis, Rheumatoid
Complement components C1q, C1r/C1s, and C1INH in rheumatoid arthritis. Correlation of in situ hybridization and northern blot results with function and protein concentration in synovium and primary cell cultures.
Arthritis, Rheumatoid
[Concentration of acute phase proteins in serum of children with rheumatoid arthritis]
Asthma
Human plasma-derived C1 esterase inhibitor concentrate has limited effect on house dust mite-induced allergic lung inflammation in mice.
Atherosclerosis
Clinical and experimental approaches to the prevention of atherosclerosis by immunological regulations.
Atherosclerosis
Distinct Longitudinal Associations of MBL, MASP-1, MASP-2, MASP-3, and MAp44 With Endothelial Dysfunction and Intima-Media Thickness: The Cohort on Diabetes and Atherosclerosis Maastricht (CODAM) Study.
Atherosclerosis
Proteomic analysis of plasma from children with sickle cell anemia and silent cerebral infarction.
Atypical Hemolytic Uremic Syndrome
The Inhibition of Complement System in Formal and Emerging Indications: Results from Parallel One-Stage Pairwise and Network Meta-Analyses of Clinical Trials and Real-Life Data Studies.
Autoimmune Diseases
Angiooedema due to acquired deficiency of C1-esterase inhibitor associated with leucocytoclastic vasculitis.
Autoimmune Diseases
Co-occurrence between C1 esterase inhibitor deficiency and autoimmune disease: a systematic literature review.
Autoimmune Diseases
Hereditary angioedema C1-esterase inhibitor replacement therapy and coexisting autoimmune disorders: findings from a claims database.
Autoimmune Diseases
Should MASP-2 Deficiency Be Considered a Primary Immunodeficiency? Relevance of the Lectin Pathway.
Bacteremia
Activation and inhibition of Hageman factor-dependent pathways and the complement system in uncomplicated bacteremia or bacterial shock.
Bacteremia
Inherited disorders of complement.
Bacteremia
Serum Concentrations of Mannan-Binding Lectin (MBL) and MBL-Associated Serine Protease-2 and the Risk of Adverse Events in Pediatric Patients With Cancer and Fever in Neutropenia.
Brain Concussion
Effect of complement C1-esterase inhibitor on brain edema and inflammation after mild traumatic brain injury in an animal model.
Brain Edema
Effect of complement C1-esterase inhibitor on brain edema and inflammation after mild traumatic brain injury in an animal model.
Brain Injuries
Changes of C1 esterase inhibitor, alpha2 globulin and sedimentation rate after severe brain injury.
Brain Injuries
Mannan binding lectin-associated serine protease-2 (MASP-2) critically contributes to post-ischemic brain injury independent of MASP-1.
Brain Injuries, Traumatic
Targeted deletions of complement lectin pathway genes improve outcome in traumatic brain injury, with MASP-2 playing a major role.
Brain Ischemia
Combination Therapy with Low-Dose IVIG and a C1-esterase Inhibitor Ameliorates Brain Damage and Functional Deficits in Experimental Ischemic Stroke.
Brain Ischemia
Mannan binding lectin-associated serine protease-2 (MASP-2) critically contributes to post-ischemic brain injury independent of MASP-1.
Capillary Leak Syndrome
Validation of C1-esterase inhibitor therapy in severe capillary leak syndrome by monitoring of extravascular lung water.
Capillary Leak Syndrome
[Idiopathic anaphylaxis]
Capillary Leak Syndrome
[Successful use of C1 esterase inhibitor in capillary leak syndrome].
Carcinogenesis
Clinical significance of mannose-binding lectin-associated serine protease-2 expression in esophageal squamous cell carcinoma.
Carcinoid Tumor
Chapter 25: Idiopathic anaphylaxis.
Carcinoid Tumor
Idiopathic anaphylaxis.
Carcinoid Tumor
[Idiopathic anaphylaxis]
Carcinoma
Clinical significance of mannose-binding lectin-associated serine protease-2 expression in esophageal squamous cell carcinoma.
Carcinoma
Complement Component 1, s Subcomponent Overexpression is an Independent Poor Prognostic Indicator in Patients with Urothelial Carcinomas of the Upper Urinary Tract and Urinary Bladder.
Carcinoma
Noncanonical Functions of C1s Complement Its Canonical Functions in Renal Cancer.
Carcinoma
Serum C1-esterase inhibitor, an essential and independent prognosticator of gastric carcinoma.
Carcinoma
Up-regulated expression of the MAT-8 gene in prostate cancer and its siRNA-mediated inhibition of expression induces a decrease in proliferation of human prostate carcinoma cells.
Carcinoma, Hepatocellular
Effect of conditioned media of acute myeloid leukemia blast cells on complement synthesis by cultured human cells of monocyte and hepatocyte origin.
Carcinoma, Hepatocellular
Hereditary haemorrhagic telangiectasia: to transplant or not to transplant - is there a right time for liver transplantation?
Carcinoma, Lobular
Elastosis in breast carcinoma: II. Association of protease inhibitors with immature elastic fibres.
Carcinoma, Non-Small-Cell Lung
The Clinical Significance of Serum MASP-2 and IDH1 in the Early Diagnosis of Non-Small Cell Lung Cancer.
Carcinoma, Renal Cell
Noncanonical Functions of C1s Complement Its Canonical Functions in Renal Cancer.
Carcinoma, Renal Cell
Unusual normolipidemic cutaneous xanthomatosis: a comparison of two cases illustrating the differential diagnosis.
Cardiomyopathies
MASP2 haplotypes are associated with high risk of cardiomyopathy in chronic Chagas disease.
Cardiovascular Diseases
MASPs at the crossroad between the complement and the coagulation cascades - the case for COVID-19.
Caroli Disease
Septic shock after liver transplantation for Caroli's disease: clinical improvement after treatment with C1-esterase inhibitor.
Cerebrovascular Disorders
MASPs at the crossroad between the complement and the coagulation cascades - the case for COVID-19.
Cervical Intraepithelial Neoplasia
MASP-1 and MASP-2 Serum Levels Are Associated With Worse Prognostic in Cervical Cancer Progression.
Chondrosarcoma
Coordinated change between complement C1s production and chondrocyte differentiation in vitro.
Chronic Urticaria
An 82-year-old man with recurrent angioedema.
Chronic Urticaria
Protease inhibitor profiles in urticaria and angio-oedema.
Chronic Urticaria
[Acquired angioedema with C1-INH deficiency and accompanying chronic spontaneous urticaria in a patient with chronic lymphatic B cell leukemia].
Coinfection
A dual role for Mannan-binding lectin-associated serine protease 2 (MASP-2) in HIV infection.
Colic
Analysis of coagulation proteins as acute-phase reactants in horses with colic.
Colitis, Ulcerative
High normal serum levels of C3 and C1 inhibitor, two acute-phase proteins belonging to the complement system, occur more frequently in patients with Crohn's disease than ulcerative colitis.
Colitis, Ulcerative
Increased titers of anti-Saccharomyces cerevisiae antibodies in Crohn's disease patients with reduced H-ficolin levels but normal MASP-2 activity.
Colorectal Neoplasms
High levels of acute phase proteins and soluble 70 kDa heat shock proteins are independent and additive risk factors for mortality in colorectal cancer.
Colorectal Neoplasms
Mannan-binding lectin (MBL) and MBL-associated serine protease 2 (MASP-2) genotypes in colorectal cancer.
Colorectal Neoplasms
Pre- and postoperative levels in serum of mannan-binding lectin associated serine protease-2 -a prognostic marker in colorectal cancer.
Colorectal Neoplasms
Serum mannan-binding lectin-associated serine protease 2 levels in colorectal cancer: relation to recurrence and mortality.
Colorectal Neoplasms
WITHDRAWN: Diagnostic performance of MASP-2 in the diagnosis of colorectal carcinoma.
Common Variable Immunodeficiency
A new subset of common variable immune deficiency characterized by reduced C1 esterase inhibitor levels.
Common Variable Immunodeficiency
Anaesthetic management of an emergency caesarean section in a complex immunologically compromised patient with pre-eclampsia and multifactorial thrombocytopaenia.
Common Variable Immunodeficiency
Recombinant Human C1 Esterase Inhibitor for the Management of Adverse Events Related to Intravenous Immunoglobulin Infusion in Patients With Common Variable Immunodeficiency or Polyneuropathy: A Pilot Open-Label Study.
complement subcomponent c1s deficiency
A Case of Angioedema Due to Acquired C1 Esterase Inhibitor Deficiency Masquerading as Suspected Peritonitis: A Case Report.
complement subcomponent c1s deficiency
Acquired C1 esterase deficiency with cold agglutinin disease associated with monoclonal IgM antibodies.
complement subcomponent c1s deficiency
Acquired C1-esterase deficiency and optic neuropathy in non-Hodgkin's lymphoma.
complement subcomponent c1s deficiency
An Unusual Case of Acquired Angioedema and Monoclonal Gammopathy of Renal Significance in a Middle-Aged Caucasian Female.
complement subcomponent c1s deficiency
Circulating levels of mannan-binding lectin (MBL) and MBL-associated serine protease 2 in endemic pemphigus foliaceus.
complement subcomponent c1s deficiency
Components of the lectin pathway of complement activation in paediatric patients of intensive care units.
complement subcomponent c1s deficiency
Deficiency of mannose-binding lectin-associated serine protease-2 associated with increased risk of fever and neutropenia in pediatric cancer patients.
complement subcomponent c1s deficiency
Emergency management of upper airway angio-oedema after routine dental extraction in a patient with C1 esterase deficiency.
complement subcomponent c1s deficiency
Extraintestinal manifestations of Edwardsiella tarda infection: a 10-year retrospective review.
complement subcomponent c1s deficiency
Falsely normal C4 in a case of acquired C1 esterase inhibitor deficiency.
complement subcomponent c1s deficiency
Functional MASP2 gene polymorphism in patients with history of rheumatic fever.
complement subcomponent c1s deficiency
Functional MASP2 single nucleotide polymorphism plays no role in psoriasis.
complement subcomponent c1s deficiency
Genetic analysis of complement C1s deficiency associated with systemic lupus erythematosus highlights alternative splicing of normal C1s gene.
complement subcomponent c1s deficiency
Hereditary angio-oedema as a rare cause of small-bowel obstruction.
complement subcomponent c1s deficiency
Hereditary C1 esterase deficiency in a Zulu kindred.
complement subcomponent c1s deficiency
Herpes simplex encephalitis in adult patients with MASP-2 deficiency.
complement subcomponent c1s deficiency
L-ficolin (ficolin-2) insufficiency is associated with combined allergic and infectious respiratory disease in children.
complement subcomponent c1s deficiency
Lectin pathway of complement activation in a Polish woman with MASP-2 deficiency.
complement subcomponent c1s deficiency
Lectin-complement pathway molecules are decreased in patients with cirrhosis and constitute the risk of bacterial infections.
complement subcomponent c1s deficiency
Mannan-binding lectin pathway deficiencies and invasive fungal infections following allogeneic stem cell transplantation.
complement subcomponent c1s deficiency
Mannan-binding lectin-associated serine protease 2 is critical for the development of renal ischemia reperfusion injury and mediates tissue injury in the absence of complement C4.
complement subcomponent c1s deficiency
Mannan-binding-lectin-associated serine proteases, characteristics and disease associations.
complement subcomponent c1s deficiency
Mannose-binding lectin and mannose-binding lectin-associated serine protease 2 in susceptibility, severity, and outcome of pneumonia in adults.
complement subcomponent c1s deficiency
Mannose-Binding Lectin and MBL-Associated Serine Protease-2 Genotypes and Serum Levels in Patients with Sporotrichosis.
complement subcomponent c1s deficiency
Molecular basis of human complement C1s deficiency.
complement subcomponent c1s deficiency
Selective complement C1s deficiency caused by homozygous four-base deletion in the C1s gene.
complement subcomponent c1s deficiency
Should MASP-2 Deficiency Be Considered a Primary Immunodeficiency? Relevance of the Lectin Pathway.
complement subcomponent c1s deficiency
Substitution therapy for C1 esterase deficiency.
complement subcomponent c1s deficiency
Targeting of mannan-binding lectin-associated serine protease-2 confers protection from myocardial and gastrointestinal ischemia/reperfusion injury.
complement subcomponent c1s deficiency
The late onset form of C1 esterase-inhibitor deficiency presenting as food allergy.
complement subcomponent c1s deficiency
The mannan-binding lectin pathway and lung disease in cystic fibrosis--disfunction of mannan-binding lectin-associated serine protease 2 (MASP-2) may be a major modifier.
complement subcomponent c1s deficiency
Tuberculosis, onychomycosis and immune deficiency in complicated Crohn's disease.
complement subcomponent c1s deficiency
[Anaesthesic management of vaginal delivery in a parturient with C1 esterase deficiency]
complement subcomponent c1s deficiency
[Angioedema of the oropharynx]
complement subcomponent c1s deficiency
[Hypocomplementemic urticarial vasculitis with glomerulopathy and renal venulitis]
Coronavirus Infections
Targeting the Complement Serine Protease MASP-2 as a Therapeutic Strategy for Coronavirus Infections.
COVID-19
C1 Esterase Inhibition: Targeting Multiple Systems in COVID-19.
COVID-19
C1 esterase inhibitor and the contact system in COVID-19.
COVID-19
Clinically distinct COVID-19 cases share notably similar immune response progression: A follow-up analysis.
COVID-19
Complement Activation in Kidneys of Patients With COVID-19.
COVID-19
Lectin Pathway Mediates Complement Activation by SARS-CoV-2 Proteins.
COVID-19
MASPs at the crossroad between the complement and the coagulation cascades - the case for COVID-19.
COVID-19
Multi-organ complement deposition in COVID-19 patients.
COVID-19
Multiple-Organ Complement Deposition on Vascular Endothelium in COVID-19 Patients.
COVID-19
Protease inhibitor plasma concentrations associate with COVID-19 infection.
COVID-19
Recombinant human C1 esterase inhibitor (conestat alfa) in the prevention of severe SARS-CoV-2 infection in hospitalized patients with COVID-19: A structured summary of a study protocol for a randomized, parallel-group, open-label, multi-center pilot trial (PROTECT-COVID-19).
COVID-19
Treatment of COVID-19 With Conestat Alfa, a Regulator of the Complement, Contact Activation and Kallikrein-Kinin System.
Crohn Disease
Dissociation between the functional activity and immunoreactive concentration of C1 esterase inhibitor in active and quiescent Crohn's disease.
Crohn Disease
High normal serum levels of C3 and C1 inhibitor, two acute-phase proteins belonging to the complement system, occur more frequently in patients with Crohn's disease than ulcerative colitis.
Crohn Disease
Increased titers of anti-Saccharomyces cerevisiae antibodies in Crohn's disease patients with reduced H-ficolin levels but normal MASP-2 activity.
Crohn Disease
[Simultaneous occurrence of hereditary angioneurotic edema and Crohn disease]
Cryoglobulinemia
Hypocomplementemic urticarial vasculitis: association with chronic obstructive pulmonary disease.
Cryoglobulinemia
Monoclonal gammopathy with significance: case series and literature review.
Cystitis, Interstitial
Serum immunoglobulin and complement alterations in interstitial cystitis.
Dermatitis, Atopic
Helicobacter pylori infection and skin diseases.
Diabetes Mellitus
Extraintestinal manifestations of Edwardsiella tarda infection: a 10-year retrospective review.
Diabetes Mellitus
Plasma Levels of MASP-1 and MASP-2 are Elevated in Type 1 Diabetes and Correlate with Glycaemic Control.
Diabetes Mellitus, Type 1
Incident microalbuminuria and complement factor mannan-binding lectin-associated protein 19 in people with newly diagnosed type 1 diabetes.
Diabetes Mellitus, Type 1
Plasma Levels of MASP-1 and MASP-2 are Elevated in Type 1 Diabetes and Correlate with Glycaemic Control.
Diabetes Mellitus, Type 2
Complement Activation and Prognosis in Patients With Type 2 Diabetes and Myocardial Infarction: A report from the DIGAMI 2 trial.
Embolism
C1 Esterase Inhibitor Activity in Amniotic Fluid Embolism.
Embolism
Practical use of C1 esterase inhibitor concentrate for clinical amniotic fluid embolism.
Embolism
Therapeutic application of C1 esterase inhibitor concentrate for clinical amniotic fluid embolism: a case report.
Embolism, Amniotic Fluid
C1 Esterase Inhibitor Activity in Amniotic Fluid Embolism.
Embolism, Amniotic Fluid
Practical use of C1 esterase inhibitor concentrate for clinical amniotic fluid embolism.
Embolism, Amniotic Fluid
Therapeutic application of C1 esterase inhibitor concentrate for clinical amniotic fluid embolism: a case report.
Encephalitis
Herpes simplex encephalitis in adult patients with MASP-2 deficiency.
Encephalitis, Herpes Simplex
Herpes simplex encephalitis in adult patients with MASP-2 deficiency.
Encephalomyelitis
Targeting the complement system in neuromyelitis optica spectrum disorder.
Encephalomyelitis, Autoimmune, Experimental
Targeting the complement system in neuromyelitis optica spectrum disorder.
Endotoxemia
C1-esterase inhibitor attenuates the inflammatory response during human endotoxemia.
Endotoxemia
Effects of C1 esterase inhibitor administration on intestinal functional capillary density, leukocyte adherence and mesenteric plasma extravasation during experimental endotoxemia.
Endotoxemia
Influence of C1-esterase inhibitor on tissue oxygenation of jejunal mucosa during endotoxemia.
Endotoxemia
The combinations C1 esterase inhibitor with coagulation factor XIII and N-acetylcysteine with tirilazad mesylate reduce the leukocyte adherence in an experimental endotoxemia in rats.
Erythema Nodosum
Complement determinations in the synovial fluid and serum of a patient with Erythema nodosum leprosum.
Esophageal Squamous Cell Carcinoma
Clinical significance of mannose-binding lectin-associated serine protease-2 expression in esophageal squamous cell carcinoma.
Food Hypersensitivity
Angioedema: frightening and frustrating.
Food Hypersensitivity
Exogenous oestrogen as an alternative to food allergy in the aetiology of angioneurotic oedema.
Food Hypersensitivity
The late onset form of C1 esterase-inhibitor deficiency presenting as food allergy.
Genetic Diseases, Inborn
A novel functional C1 inhibitor activity assay in dried blood spot for diagnosis of Hereditary angioedema.
Genetic Diseases, Inborn
A robust multiplexed assay to quantify C1-inhibitor, C1q, and C4 proteins for in vitro diagnosis of hereditary angioedema from dried blood spot.
Genetic Diseases, Inborn
Administration of conestat alfa, human C1 esterase inhibitor and icatibant in the treatment of acute angioedema attacks in adults with hereditary angioedema due to C1 esterase inhibitor deficiency. Treatment comparison based on systematic review results.
Genetic Diseases, Inborn
An investigational RNAi therapeutic targeting Factor XII (ALN-F12) for the treatment of hereditary angioedema.
Genetic Diseases, Inborn
An update on the diagnosis and management of hereditary angioedema with abnormal c1 inhibitor.
Genetic Diseases, Inborn
HAE update: epidemiology and burden of disease.
Genetic Diseases, Inborn
Hereditary angioedema: a clinical review for the otolaryngologist.
Genetic Diseases, Inborn
Hereditary angioedema: an update on causes, manifestations and treatment.
Genetic Diseases, Inborn
Hereditary angioedema: imaging manifestations and clinical management.
Genetic Diseases, Inborn
Hereditary angioedema: not an allergy.
Genetic Diseases, Inborn
Hereditary angioedema: quality of life in Brazilian patients.
Genetic Diseases, Inborn
Icatibant. Attacks of hereditary angioedema: continue to use C1 esterase inhibitor.
Genetic Diseases, Inborn
Long-Term Prophylaxis of Hereditary Angioedema with a Pasteurized C1 Inhibitor Concentrate.
Genetic Diseases, Inborn
Management of patients with hereditary angio-oedema in dental, oral, and maxillofacial surgery: a review.
Genetic Diseases, Inborn
Peri-operative management of a patient with hereditary angioedema undergoing laparoscopic cholecystectomy.
Genetic Diseases, Inborn
Perioperative management of tooth extractions for a patient with hereditary angioedema.
Genetic Diseases, Inborn
Recognition, Evaluation, and Management of Pediatric Hereditary Angioedema.
Genetic Diseases, Inborn
Recombinant human C1 esterase inhibitor in the management of hereditary angioedema.
Genetic Diseases, Inborn
Successful anesthetic management during abdominal wall-lifting laparoscopic cholecystectomy in a patient with hereditary angioedema.
Genetic Diseases, Inborn
Successful management of hereditary angioedema during tonsillectomy: a case report.
Genetic Diseases, Inborn
Successful resolution of bowel obstruction in a patient with hereditary angioedema.
Genetic Diseases, Inborn
Treatment with C1-esterase inhibitor concentrate in type I or II hereditary angioedema: a systematic literature review.
Glioblastoma
Construction of a competitive endogenous RNA network and analysis of potential regulatory axis targets in glioblastoma.
Glioblastoma
The Role of C1-Esterase Inhibitors in the Management of Vasogenic Edema in Glioblastoma.
Glioma
Increased expression and secretion of r-Gsp protein, rat counterpart of complement C1s precursor, during cyclic AMP-induced differentiation in rat C6 glioma cells.
Glomerulonephritis
Hereditary angioneurotic edema: immunochemical 'activity' without clinical expression.
Glomerulonephritis
Monoclonal gammopathy with significance: case series and literature review.
Glomerulonephritis
[Hereditary deficiency of C1 esterase inhibitor. Lupus and glomerulonephritis]
Glomerulonephritis, IGA
Safety, Tolerability and Efficacy of Narsoplimab, a Novel MASP-2 Inhibitor for the Treatment of IgA Nephropathy.
Glycogen Storage Disease
Budgetary Impact of Medicinal Therapies for Rare Diseases in Bulgaria.
Granuloma
Construction of human MASP-2-CCP1/2SP, CCP2SP, SP plasmid DNA nanolipoplexes and the effects on tuberculosis in BCG-infected mice.
Granuloma
Effects of hMASP-2 on the formation of BCG infection-induced granuloma in the lungs of BALB/c mice.
Guillain-Barre Syndrome
Guillain-Barré syndrome following danazol and corticosteroid therapy for hereditary angioedema.
Hearing Loss, Noise-Induced
Transcriptome characterization by RNA-Seq reveals the involvement of the complement components in noise-traumatized rat cochleae.
Heart Arrest
The complement lectin pathway after cardiac arrest.
Hematologic Neoplasms
Prognosis in pediatric hematologic malignancies is associated with serum concentration of mannose-binding lectin-associated serine protease-2 (MASP-2).
Hemoglobinuria
Biphenylsulfonyl-thiophene-carboxamidine inhibitors of the complement component C1s.
Hemoglobinuria
Complement blockade with a C1 esterase inhibitor in paroxysmal nocturnal hemoglobinuria.
Hemoglobinuria
Targeting the complement system in neuromyelitis optica spectrum disorder.
Hemoglobinuria
The Inhibition of Complement System in Formal and Emerging Indications: Results from Parallel One-Stage Pairwise and Network Meta-Analyses of Clinical Trials and Real-Life Data Studies.
Hemoglobinuria, Paroxysmal
Biphenylsulfonyl-thiophene-carboxamidine inhibitors of the complement component C1s.
Hemoglobinuria, Paroxysmal
Complement blockade with a C1 esterase inhibitor in paroxysmal nocturnal hemoglobinuria.
Hemoglobinuria, Paroxysmal
Targeting the complement system in neuromyelitis optica spectrum disorder.
Hemoglobinuria, Paroxysmal
The Inhibition of Complement System in Formal and Emerging Indications: Results from Parallel One-Stage Pairwise and Network Meta-Analyses of Clinical Trials and Real-Life Data Studies.
Hemolytic-Uremic Syndrome
Activation of both coagulation and fibrinolysis in childhood hemolytic uremic syndrome.
Hepatic Veno-Occlusive Disease
Hepatic veno-occlusive disease with severe capillary leakage after peripheral stem cell transplantation: treatment with recombinant plasminogen activator and C1-esterase inhibitor concentrate.
Hepatitis
Effects of MASP2 haplotypes and MASP-2 levels in hepatitis C-infected patients.
Hepatitis B
Contributions to the optimal use of human blood. IX. Elimination of hepatitis B transmission by (potentially) infectious plasma derivatives.
Hepatitis B
Hypocomplementemic urticarial vasculitis: association with chronic obstructive pulmonary disease.
Hepatitis C
Effects of MASP2 haplotypes and MASP-2 levels in hepatitis C-infected patients.
Hepatitis C
MASP2 gene polymorphism is associated with susceptibility to hepatitis C virus infection.
Hereditary Angioedema Types I and II
A case of hereditary angioedema associated with idiopathic hypoparathyroidism.
Hereditary Angioedema Types I and II
An Unusual Case of Acquired Angioedema and Monoclonal Gammopathy of Renal Significance in a Middle-Aged Caucasian Female.
Hereditary Angioedema Types I and II
Anaesthesia Management of a Patient with Hereditary Angioedema with Prophylactic Administration of C1 Esterase Inhibitor: Case report and literature review.
Hereditary Angioedema Types I and II
C1 esterase inhibitor activity is reduced in the acute phase following burn injury: a prospective observational study.
Hereditary Angioedema Types I and II
Capillary leak syndrome and disseminated intravascular coagulation after kidney transplantation in a patient with hereditary angioedema - A case report.
Hereditary Angioedema Types I and II
Cinryze as the first approved C1 inhibitor in the USA for the treatment of hereditary angioedema: approval, efficacy and safety.
Hereditary Angioedema Types I and II
Clinical presentation and diagnosis of hereditary angio-oedema in five families.
Hereditary Angioedema Types I and II
Complement abnormalities in diffuse plane xanthomatosis with paraproteinaemia.
Hereditary Angioedema Types I and II
Cutaneous manifestations of complement deficiencies.
Hereditary Angioedema Types I and II
Diagnosis and screening of patients with hereditary angioedema in primary care.
Hereditary Angioedema Types I and II
Diminished capacity of opsonization and immune complex solubilization, and detection of anti-C1q antibodies in sera from patients with hereditary angioedema.
Hereditary Angioedema Types I and II
DX-88 and HAE: a developmental perspective.
Hereditary Angioedema Types I and II
Ecallantide for the treatment of hereditary angiodema in adults.
Hereditary Angioedema Types I and II
Efficacy Assessments in Randomized Controlled Studies of Acute Therapy for Hereditary Angioedema.
Hereditary Angioedema Types I and II
Exacerbation of a lupus-erythematosus-like syndrome during treatment of non-C1-esterase-inhibitor-dependent angioedema with danazol.
Hereditary Angioedema Types I and II
General anaesthetic for a pilonidal sinus excision in a patient with hereditary angio-oedema.
Hereditary Angioedema Types I and II
Glomerulonephritis and hereditary angioedema: report of 2 cases.
Hereditary Angioedema Types I and II
Hereditary angioedema and pregnancy: successful management of recurrent and frequent attacks of angioedema with C1-inhibitor concentrate, danazol and tranexamic acid - a case report.
Hereditary Angioedema Types I and II
Hereditary angioedema type II--a study of two families.
Hereditary Angioedema Types I and II
Hereditary angioedema: a Taiwanese family with a novel gene mutation.
Hereditary Angioedema Types I and II
Hereditary angioedema: an update on causes, manifestations and treatment.
Hereditary Angioedema Types I and II
Hereditary angioedema: therapeutic effect of danazol on C4 and C1 esterase inhibitors.
Hereditary Angioedema Types I and II
Inherited disorders of complement.
Hereditary Angioedema Types I and II
Is there a need for clinical guidelines in the United States for the diagnosis of hereditary angioedema and the screening of family members of affected patients?
Hereditary Angioedema Types I and II
Long-Term Prophylaxis of Hereditary Angioedema with a Pasteurized C1 Inhibitor Concentrate.
Hereditary Angioedema Types I and II
Modern preoperative and intraoperative management of hereditary angioedema.
Hereditary Angioedema Types I and II
Modification of peripheral blood T-lymphocyte surface receptors and Langerhans cell numbers in hereditary angioedema.
Hereditary Angioedema Types I and II
Participation of Hageman factor dependent pathways in human disease states.
Hereditary Angioedema Types I and II
Prospective study of C1 esterase inhibitor in the treatment of successive acute abdominal and facial hereditary angioedema attacks.
Hereditary Angioedema Types I and II
Recognition, Evaluation, and Management of Pediatric Hereditary Angioedema.
Hereditary Angioedema Types I and II
Successful treatment of acute hereditary angioedema attacks with self-administered icatibant in patients with venous access problems.
Hereditary Angioedema Types I and II
The complex alteration in the network of IL-17-type cytokines in patients with hereditary angioedema.
Hereditary Angioedema Types I and II
The late onset form of C1 esterase-inhibitor deficiency presenting as food allergy.
Hereditary Angioedema Types I and II
treatment of hereditary angio-oedema by low dose attenuated androgens: disassociation of clinical response from levels of C1 esterase inhibitor and C4.
Hereditary Angioedema Types I and II
Type I hereditary angioedema in Taiwan -- clinical, biological features and genetic study.
Hereditary Angioedema Types I and II
[A study of coagulation contact factors in hereditary angioneurotic oedema (author's transl)]
Hereditary Angioedema Types I and II
[Acquired angioneurotic edema caused by acquired deficiency of C1 esterase inhibitor disclosing lymphoproliferative syndrome. Apropos of a case, review of the literature]
Hereditary Angioedema Types I and II
[Acquired deficiency of C1 esterase inhibitor and malignant lymphoproliferative syndromes]
Hereditary Angioedema Types I and II
[Acquired deficiency of C1 esterase inhibitor, persistent eyelid edema and subcutaneous lupus erythematosus]
Hereditary Angioedema Types I and II
[Clinical symptoms and therapy of the hereditary angioneurotic edema (author's transl)]
Hereditary Angioedema Types I and II
[Correction of deficiency of C1 esterase inhibitor in angioneurotic edema with oxymetholone]
Hereditary Angioedema Types I and II
[Hereditary angioedema caused by a deficiency of C1 esterase inhibitor. A sporadic case of late appearance]
Hereditary Angioedema Types I and II
[Hereditary angioedema, a rare cause of recurrent abdominal pains. A report of 2 clinical cases and comments of a general nature]
Hereditary Angioedema Types I and II
[Hereditary angioedema]
Hereditary Angioedema Types I and II
[Hereditary deficiency of C1 esterase inhibitor. Lupus and glomerulonephritis]
Hereditary Angioedema Types I and II
[Idiopathic anaphylaxis]
Hereditary Angioedema Types I and II
[Immune complex nephropathy and hereditary deficiency of C1 esterase inhibitor (author's transl)]
Hereditary Angioedema Types I and II
[Recurrent attacks of angioedema ascribed to the use of estrogen preparations and a pregnancy (hereditary angioedema type 3)]
Hereditary Angioedema Types I and II
[Respiratory manifestations in hereditary angioneurotic edema]
Hereditary Angioedema Types I and II
[Therapeutic approach of hereditary angioedema]
Hereditary Complement Deficiency Diseases
Glomerulonephritis and hereditary angioedema: report of 2 cases.
Hereditary Complement Deficiency Diseases
[Acquired angioneurotic edema caused by acquired deficiency of C1 esterase inhibitor disclosing lymphoproliferative syndrome. Apropos of a case, review of the literature]
Hereditary Complement Deficiency Diseases
[Immune complex nephropathy and hereditary deficiency of C1 esterase inhibitor (author's transl)]
HIV Infections
A dual role for Mannan-binding lectin-associated serine protease 2 (MASP-2) in HIV infection.
Hypersensitivity
Allergenicity and safety of recombinant human C1 esterase inhibitor in patients with allergy to rabbit or cow's milk.
Hypersensitivity
Allergic urticaria and hereditary angioedema. Independent association in the same patient.
Hypersensitivity
Serum concentrations of lectin-pathway components in healthy neonates, children and adults: mannan-binding lectin (MBL), M-, L-, and H-ficolin, and MBL-associated serine protease-2 (MASP-2).
Hypertension
MASPs at the crossroad between the complement and the coagulation cascades - the case for COVID-19.
Hypotension
Inhibition of the hypotensive effect of plasma protein solutions by C1 esterase inhibitor.
IgA Deficiency
Urticarial vasculitis, IgA deficiency and C1 esterase inhibitor deficiency in the presence of an IgG monoclonal gammopathy--a case report.
Infarction, Middle Cerebral Artery
Protective effect of C1 esterase inhibitor on reperfusion injury in the rat middle cerebral artery occlusion model.
Infections
A dual role for Mannan-binding lectin-associated serine protease 2 (MASP-2) in HIV infection.
Infections
Acquired C1-esterase inhibitor deficiency and recurrent herpes infection in a patient with chronic lymphocytic leukemia.
Infections
Angioedema due to acquired C1-esterase inhibitor deficiency in a patient with Helicobacter pylori infection.
Infections
Angiooedema due to acquired deficiency of C1-esterase inhibitor associated with leucocytoclastic vasculitis.
Infections
Association between MASP-2 gene polymorphism and risk of infection diseases: A meta-analysis.
Infections
Association of MASP-2 Levels and MASP2 Gene Polymorphisms with Rheumatoid Arthritis in Patients and Their Relatives.
Infections
C1 esterase inhibitor and the contact system in COVID-19.
Infections
C1 esterase inhibitor: new preparation. A major advance in emergency treatment of hereditary angioneurotic oedema.
Infections
Cleavage of kininogen and subsequent bradykinin release by the complement component: mannose-binding lectin-associated serine protease (MASP)-1.
Infections
Complement C1 esterase inhibitor levels linked to infections and contaminated heparin-associated adverse events.
Infections
Construction of human MASP-2-CCP1/2SP, CCP2SP, SP plasmid DNA nanolipoplexes and the effects on tuberculosis in BCG-infected mice.
Infections
Deficiency of mannose-binding lectin-associated serine protease-2 associated with increased risk of fever and neutropenia in pediatric cancer patients.
Infections
Effects of MASP2 haplotypes and MASP-2 levels in hepatitis C-infected patients.
Infections
Extraintestinal manifestations of Edwardsiella tarda infection: a 10-year retrospective review.
Infections
Impact of the complement lectin pathway on cytomegalovirus disease early after kidney transplantation.
Infections
Inherited disorders of complement.
Infections
L-ficolin (ficolin-2) insufficiency is associated with combined allergic and infectious respiratory disease in children.
Infections
Lack of association between polymorphisms of MASP2 and susceptibility to SARS coronavirus infection.
Infections
Low MBL-associated serine protease 2 (MASP-2) levels correlate with urogenital schistosomiasis in Nigerian children.
Infections
M-ficolin levels are associated with the occurrence of severe infections in patients with haematological cancer undergoing chemotherapy.
Infections
Mannan-binding lectin-associated serine protease-2 (MASP-2) in a large cohort of neonates and its clinical associations.
Infections
Pharmaceutical approval update.
Infections
Serum mannan-binding lectin-associated serine protease 2 levels in colorectal cancer: relation to recurrence and mortality.
Infections
Tuberculosis, onychomycosis and immune deficiency in complicated Crohn's disease.
Intestinal Obstruction
Recurrent intestinal obstruction with acquired angio-oedema, due to C1-esterase inhibitor deficiency.
Intussusception
Colonic Intussusception Secondary to Hereditary Angioedema.
Intussusception
Hereditary Angioedema and Gastrointestinal Complications: An Extensive Review of the Literature.
Ischemic Stroke
Combination Therapy with Low-Dose IVIG and a C1-esterase Inhibitor Ameliorates Brain Damage and Functional Deficits in Experimental Ischemic Stroke.
Ischemic Stroke
Serine proteases of the complement lectin pathway and their genetic variations in ischaemic stroke.
Ischemic Stroke
Tissue Plasminogen Activator-Induced Angioedema Involving a Posterior Cerebral Artery Infarct: A Case Presentation.
Kidney Neoplasms
Complement C1s and C4d as Prognostic Biomarkers in Renal Cancer: Emergence of Noncanonical Functions of C1s.
Laryngeal Edema
Asphyxiation by laryngeal edema in patients with hereditary angioedema.
Laryngeal Edema
Clinical studies of sudden upper airway obstruction in patients with hereditary angioedema due to C1 esterase inhibitor deficiency.
Laryngeal Edema
Hereditary angioedema presenting as epiglottitis.
Laryngeal Edema
Nanofiltered C1 esterase inhibitor for treatment of laryngeal attacks in patients with hereditary angioedema.
Laryngeal Edema
Treatment with C1-esterase inhibitor concentrate in type I or II hereditary angioedema: a systematic literature review.
Laryngismus
[Croup syndrome]
Leprosy
Leprosy association with low MASP-2 levels generated by MASP2 haplotypes and polymorphisms flanking MAp19 exon 5.
Leukemia
Association between serum levels of MASP-2 and neutropenic febrile attacks in children with leukemia.
Leukemia
Unusual normolipidemic cutaneous xanthomatosis: a comparison of two cases illustrating the differential diagnosis.
Leukemia, Lymphocytic, Chronic, B-Cell
Acquired C1-esterase inhibitor deficiency and recurrent herpes infection in a patient with chronic lymphocytic leukemia.
Leukemia, Lymphocytic, Chronic, B-Cell
Lymphocytic lymphoma and acquired C1 esterase inhibitor deficiency.
Leukemia, Lymphocytic, Chronic, B-Cell
Refractory Abdominal Pain in a Patient with Chronic Lymphocytic Leukemia: Be Wary of Acquired Angioedema due to C1 Esterase Inhibitor Deficiency.
Leukemia, Myeloid, Acute
Effect of conditioned media of acute myeloid leukemia blast cells on complement synthesis by cultured human cells of monocyte and hepatocyte origin.
Leukopenia
Necrobiotic xanthogranuloma with paraproteinemia. A review of 22 cases.
Lung Diseases
The Clinical Significance of Serum MASP-2 and IDH1 in the Early Diagnosis of Non-Small Cell Lung Cancer.
Lung Diseases
The mannan-binding lectin pathway and lung disease in cystic fibrosis--disfunction of mannan-binding lectin-associated serine protease 2 (MASP-2) may be a major modifier.
Lung Injury
Antihistone Properties of C1 Esterase Inhibitor Protect against Lung Injury.
Lung Injury
Effect of complement fragment 1 esterase inhibition on survival of human decay-accelerating factor pig lungs perfused with human blood.
Lung Injury
Nebulized C1-Esterase Inhibitor does not Reduce Pulmonary Complement Activation in Rats with Severe Streptococcus Pneumoniae Pneumonia.
Lung Injury
Plasma-Derived Human C1-Esterase Inhibitor Does Not Prevent Mechanical Ventilation-Induced Pulmonary Complement Activation in a Rat Model of Streptococcus pneumoniae Pneumonia.
Lung Injury
Targeting the Complement Serine Protease MASP-2 as a Therapeutic Strategy for Coronavirus Infections.
Lung Neoplasms
Limited proteolysis of beta 2-microglobulin at Lys-58 by complement component C1s.
Lung Neoplasms
The Clinical Significance of Serum MASP-2 and IDH1 in the Early Diagnosis of Non-Small Cell Lung Cancer.
Lung Neoplasms
[A case of lung cancer with hereditary angioedema treated effectively by chemo-radiotherapy with C1 esterase inhibitor concentrate and danazol]
Lupus Erythematosus, Systemic
CT Findings of Acute Small-Bowel Entities.
Lupus Erythematosus, Systemic
Facial angioedema and systemic lupus erythematosus: case report.
Lupus Erythematosus, Systemic
Genetic analysis of complement C1s deficiency associated with systemic lupus erythematosus highlights alternative splicing of normal C1s gene.
Lupus Erythematosus, Systemic
Human parvovirus infection: rheumatic manifestations, angioedema, C1 esterase inhibitor deficiency, ANA positivity, and possible onset of systemic lupus erythematosus.
Lupus Erythematosus, Systemic
Hypocomplementemic urticarial vasculitis: association with chronic obstructive pulmonary disease.
Lupus Erythematosus, Systemic
Intractable acquired autoimmune angioedema in a patient with systemic lupus erythematosus.
Lupus Erythematosus, Systemic
The lectin complement pathway serine proteases (MASPs) represent a possible crossroad between the coagulation and complement systems in thromboinflammation.
Lupus Nephritis
Gene Expression Analysis Detected a Low Expression Level of C1s Gene in ICR-Derived Glomerulonephritis (ICGN) Mice.
Lymphoma
Acquired C1 esterase inhibitor deficiency in a marginal zone lymphoma patient treated with rituximab.
Lymphoma
Acquired C1 esterase inhibitor deficiency in lymphomas: prevalence, symptoms, and response to treatment.
Lymphoma
Angioedema in the emergency department: a presentation of lymphoma.
Lymphoma
C1 esterase inhibitor as a possible tumour marker in malignant lymphoma.
Lymphoma
C1-esterase inhibitor autoantibodies in a patient with acute tongue swelling.
Lymphoma
Intestinal angioedema caused by an acquired C1 esterase inhibitor deficiency associated with underlying splenic marginal zone lymphoma.
Lymphoma
Long-standing angioedema with C1 esterase inhibitor deficiency associated with occult lymphoma.
Lymphoma
Lupus anticoagulant and thrombosis in splenic marginal zone lymphoma.
Lymphoma
Prognosis in pediatric hematologic malignancies is associated with serum concentration of mannose-binding lectin-associated serine protease-2 (MASP-2).
Lymphoma
Spontaneous regression of acquired C1 esterase inhibitor deficiency associated with splenic marginal zone lymphoma presenting with recurrent angio-oedema.
Lymphoma
Urticarial vasculitis and asymptomatic acquired C1 esterase inhibitor deficiency revealing an angioimmunoblastic T cell lymphoma.
Lymphoma
[Acquired C1 esterase inhibitor deficiency and lymphoproliferative syndromes]
Lymphoma
[Acquired C1 esterase inhibitor deficiency, Gougerot-Sjögren syndrome and B lymphoma]
Lymphoma
[Acquired C1-esterase inhibitor deficiency with angioedema in lymphoplasmocytic lymphoma]
Lymphoma
[Apropos of the case reported by M. Leporrier et al., on mixed nodular lymphoma associated with a deficiency of C1-esterase inhibitor]
Lymphoma, B-Cell
Acquired C1-esterase inhibitor deficiency and positive lupus anticoagulant accompanied by splenic marginal zone B-cell lymphoma.
Lymphoma, B-Cell, Marginal Zone
Acquired C1-esterase inhibitor deficiency and positive lupus anticoagulant accompanied by splenic marginal zone B-cell lymphoma.
Lymphoma, Follicular
[Apropos of the case reported by M. Leporrier et al., on mixed nodular lymphoma associated with a deficiency of C1-esterase inhibitor]
Lymphoma, Follicular
[Mixed nodular lymphoma in association with a C1 esterase inhibitor deficiency (author's transl)]
Lymphoma, Non-Hodgkin
Acquired C1-esterase deficiency and optic neuropathy in non-Hodgkin's lymphoma.
Lymphoma, Non-Hodgkin
Lupus anticoagulant and thrombosis in splenic marginal zone lymphoma.
Lymphoma, T-Cell
Urticarial vasculitis and asymptomatic acquired C1 esterase inhibitor deficiency revealing an angioimmunoblastic T cell lymphoma.
Lymphoma, T-Cell, Peripheral
Pharmaceutical approval update.
Lymphoproliferative Disorders
Acquired angioedema.
Lymphoproliferative Disorders
Acquired angioedema: Autoantibody associations and C1q utility as a diagnostic tool.
Lymphoproliferative Disorders
Acquired C1 esterase inhibitor deficiency as manifestation of T-cell lymphoproliferative disorder.
Lymphoproliferative Disorders
Acquired C1 esterase inhibitor deficiency or serendipity? The chance finding of a paraprotein after an apparently low C1 esterase inhibitor concentration.
Lymphoproliferative Disorders
Acquired C1 esterase inhibitor deficiency.
Lymphoproliferative Disorders
Angioedema as the first presentation of B-cell non-Hodgkin lymphoma--an unusual case with normal C1 esterase inhibitor level: a case report.
Lymphoproliferative Disorders
Angiooedema due to acquired deficiency of C1-esterase inhibitor associated with leucocytoclastic vasculitis.
Lymphoproliferative Disorders
Antiepileptic drug-induced lymphoproliferative disorder associated with acquired C1 esterase inhibitor deficiency and angioedema.
Macroglossia
Angioedema of the tongue due to acquired C1 esterase inhibitor deficiency.
Mania
Are Mannan-binding Lectine Serin Protease-2 and Alpha-1-microglobulin and Bukinin Precursor the Potential Biomarkers of Manic Episode? A Study via Urinary Proetomic Analysis.
Mastocytosis
[Idiopathic anaphylaxis]
Mastocytosis, Systemic
Chapter 25: Idiopathic anaphylaxis.
Mastocytosis, Systemic
Idiopathic anaphylaxis.
Memory Disorders
Early treatment with C1 esterase inhibitor improves weight but not memory deficits in a rat model of status epilepticus.
Meningitis, Bacterial
Mannose-binding lectin-associated serine protease 2 (MASP-2) contributes to poor disease outcome in humans and mice with pneumococcal meningitis.
Meningitis, Pneumococcal
Mannose-binding lectin-associated serine protease 2 (MASP-2) contributes to poor disease outcome in humans and mice with pneumococcal meningitis.
Multiple Sclerosis
Gene-environment interactions in multiple sclerosis: innate and adaptive immune responses to human endogenous retrovirus and herpesvirus antigens and the lectin complement activation pathway.
Multiple Sclerosis
Mannose binding lectin mediated complement pathway in multiple sclerosis.
Mycoses
Mannose-Binding Lectin and MBL-Associated Serine Protease-2 Genotypes and Serum Levels in Patients with Sporotrichosis.
Myocardial Infarction
Administration of C1-esterase inhibitor during emergency coronary artery bypass surgery in acute ST-elevation myocardial infarction.
Myocardial Infarction
Beneficial effects of C1 esterase inhibitor in ST-elevation myocardial infarction in patients who underwent surgical reperfusion: a randomised double-blind study.
Myocardial Infarction
Myocardial infarction induces atrial inflammation that can be prevented by C1-esterase inhibitor.
Myocardial Infarction
TFPI inhibits lectin pathway of complement activation by direct interaction with MASP-2.
Myocardial Ischemia
Cardioprotective effects of a C1 esterase inhibitor in myocardial ischemia and reperfusion.
Myocardial Ischemia
MASP-2 activation is involved in ischemia-related necrotic myocardial injury in humans.
Myocardial Ischemia
Rescue therapy with C1-esterase inhibitor concentrate after emergency coronary surgery for failed PTCA.
Myocardial Reperfusion Injury
Beneficial effects of C1 esterase inhibitor in ST-elevation myocardial infarction in patients who underwent surgical reperfusion: a randomised double-blind study.
Nasal Obstruction
[Hereditary angioedema due to C1-esterase inhibitor deficiency]
Neoplasm Metastasis
Clinical significance of mannose-binding lectin-associated serine protease-2 expression in esophageal squamous cell carcinoma.
Neoplasm Metastasis
[Proteinase inhibitors and fibrinogen split products in patients with malignant diseases (author's transl)]
Neoplasms
Acquired C1 esterase inhibitor deficiency or serendipity? The chance finding of a paraprotein after an apparently low C1 esterase inhibitor concentration.
Neoplasms
Acquired C1 esterase inhibitor deficiency: An atypical first presentation intra-operatively.
Neoplasms
Acquired C1 inhibitor deficiency: postmortem diagnosis.
Neoplasms
Angioedema of the tongue due to acquired C1 esterase inhibitor deficiency.
Neoplasms
Angiooedema due to acquired deficiency of C1-esterase inhibitor associated with leucocytoclastic vasculitis.
Neoplasms
Antithrombin III, but not C1 esterase inhibitor reduces inflammatory response in lipopolysaccharide-stimulated human monocytes in an ex-vivo whole blood setting.
Neoplasms
C1 esterase inhibitor as a possible tumour marker in malignant lymphoma.
Neoplasms
C1 esterase inhibitor protein associated with human cancer: a tumour marker.
Neoplasms
C1-esterase inactivator from cancer cells is C-reactive protein.
Neoplasms
Clinical significance of mannose-binding lectin-associated serine protease-2 expression in esophageal squamous cell carcinoma.
Neoplasms
Deficiency of mannose-binding lectin-associated serine protease-2 associated with increased risk of fever and neutropenia in pediatric cancer patients.
Neoplasms
Effect of tumour necrosis factor-alpha on proliferation, activation and protein synthesis of rat hepatic stellate cells.
Neoplasms
Human cytokine responses to coronary artery bypass grafting with and without cardiopulmonary bypass.
Neoplasms
Mannan-binding lectin (MBL) and MBL-associated serine protease-2 in children with cancer.
Neoplasms
Mannose-Binding Lectin (MBL) and MBL-associated serine protease-2 (MASP-2) in women with malignant and benign ovarian tumours.
Neoplasms
MASP-1 and MASP-2 Serum Levels Are Associated With Worse Prognostic in Cervical Cancer Progression.
Neoplasms
Microheterogeneous changes of the C1-esterase inhibitor in plasma cannot predict operability, postoperative complications, or recurrence in cancer surgery.
Neoplasms
Pre- and postoperative levels in serum of mannan-binding lectin associated serine protease-2 -a prognostic marker in colorectal cancer.
Neoplasms
Pre-operative plasma levels of C-reactive protein, albumin and various plasma protease inhibitors for the pre-operative assessment of operability and recurrence in cancer surgery.
Neoplasms
Prognosis in pediatric hematologic malignancies is associated with serum concentration of mannose-binding lectin-associated serine protease-2 (MASP-2).
Neoplasms
Serum Concentrations of Mannan-Binding Lectin (MBL) and MBL-Associated Serine Protease-2 and the Risk of Adverse Events in Pediatric Patients With Cancer and Fever in Neutropenia.
Neoplasms
Serum mannan-binding lectin-associated serine protease 2 levels in colorectal cancer: relation to recurrence and mortality.
Neoplasms
The Clinical Significance of Serum MASP-2 and IDH1 in the Early Diagnosis of Non-Small Cell Lung Cancer.
Neoplasms
Up-regulated expression of the MAT-8 gene in prostate cancer and its siRNA-mediated inhibition of expression induces a decrease in proliferation of human prostate carcinoma cells.
Neoplasms
Useful laboratory tests for studying thrombogenesis in acute cardiac syndromes.
Neoplasms
[Croup syndrome]
Neoplasms
[Proteinase inhibitors and fibrinogen split products in patients with malignant diseases (author's transl)]
Nephritis
Guillain-Barré syndrome following danazol and corticosteroid therapy for hereditary angioedema.
Nephrotic Syndrome
Monoclonal gammopathy with significance: case series and literature review.
Neuromyelitis Optica
Potential therapeutic benefit of C1-esterase inhibitor in neuromyelitis optica evaluated in vitro and in an experimental rat model.
Neuromyelitis Optica
Purified human C1-esterase inhibitor is safe in acute relapses of neuromyelitis optica.
Neuromyelitis Optica
Targeting the complement system in neuromyelitis optica spectrum disorder.
Neutropenia
Deficiency of mannose-binding lectin-associated serine protease-2 associated with increased risk of fever and neutropenia in pediatric cancer patients.
Neutropenia
Necrobiotic xanthogranuloma with paraproteinemia. A review of 22 cases.
Neutropenia
Serum Concentrations of Mannan-Binding Lectin (MBL) and MBL-Associated Serine Protease-2 and the Risk of Adverse Events in Pediatric Patients With Cancer and Fever in Neutropenia.
Obesity
Contact activated kallikrein generation is reduced six months after gastric bypass.
Onychomycosis
Tuberculosis, onychomycosis and immune deficiency in complicated Crohn's disease.
Optic Nerve Diseases
Acquired C1-esterase deficiency and optic neuropathy in non-Hodgkin's lymphoma.
Ovarian Neoplasms
Mannose-Binding Lectin (MBL) and MBL-associated serine protease-2 (MASP-2) in women with malignant and benign ovarian tumours.
Pancreatitis
Adjuvant treatment of severe acute pancreatitis with C1 esterase inhibitor concentrate after haematopoietic stem cell transplantation.
Pancreatitis
Combined treatment with C1 esterase inhibitor and antithrombin III improves survival in severe acute experimental pancreatitis.
Pancreatitis
Effects of C1-esterase inhibitor in three models of acute pancreatitis.
Pancreatitis, Acute Hemorrhagic
Effects of C1-esterase inhibitor in three models of acute pancreatitis.
Paralysis
[Croup syndrome]
Paraproteinemias
Monoclonal gammopathy with significance: case series and literature review.
Paraproteinemias
Unusual normolipidemic cutaneous xanthomatosis: a comparison of two cases illustrating the differential diagnosis.
Paraproteinemias
Urticarial vasculitis in a connective tissue disease clinic: patterns, presentations, and treatment.
Paraproteinemias
[Idiopathic anaphylaxis]
Parvoviridae Infections
Human parvovirus infection: rheumatic manifestations, angioedema, C1 esterase inhibitor deficiency, ANA positivity, and possible onset of systemic lupus erythematosus.
Peritonitis
A Case of Angioedema Due to Acquired C1 Esterase Inhibitor Deficiency Masquerading as Suspected Peritonitis: A Case Report.
Persistent Infection
The mannan-binding lectin pathway and lung disease in cystic fibrosis--disfunction of mannan-binding lectin-associated serine protease 2 (MASP-2) may be a major modifier.
Persistent Vegetative State
Association of Lectin Pathway Protein Levels and Genetic Variants Early after Injury with Outcomes after Severe Traumatic Brain Injury: A Prospective Cohort Study.
Pheochromocytoma
Chapter 25: Idiopathic anaphylaxis.
Pheochromocytoma
Idiopathic anaphylaxis.
Pneumococcal Infections
The lectin pathway of complement activation is a critical component of the innate immune response to pneumococcal infection.
Pneumonia
Human plasma-derived C1 esterase inhibitor concentrate has limited effect on house dust mite-induced allergic lung inflammation in mice.
Pneumonia
Mannan-binding lectin (MBL) and MBL-associated serine protease 2 (MASP-2) genotypes in colorectal cancer.
Pneumonia
Nebulized C1-Esterase Inhibitor does not Reduce Pulmonary Complement Activation in Rats with Severe Streptococcus Pneumoniae Pneumonia.
Pneumonia
Plasma-Derived Human C1-Esterase Inhibitor Does Not Prevent Mechanical Ventilation-Induced Pulmonary Complement Activation in a Rat Model of Streptococcus pneumoniae Pneumonia.
Pneumonia
Serum mannan-binding lectin-associated serine protease 2 levels in colorectal cancer: relation to recurrence and mortality.
Polyneuropathies
Recombinant Human C1 Esterase Inhibitor for the Management of Adverse Events Related to Intravenous Immunoglobulin Infusion in Patients With Common Variable Immunodeficiency or Polyneuropathy: A Pilot Open-Label Study.
Pre-Eclampsia
C1-esterase inhibitor in uncomplicated pregnancy and mild and moderate preeclampsia.
Primary Myelofibrosis
Correction of recurrent angioedema related to C1 esterase inhibitor deficiency as a secondary event following nonmyeloablative allogeneic stem cell transplantation in a patient with myelofibrosis.
Proteinuria
Absence of the Lectin Activation Pathway of Complement Ameliorates Proteinuria-Induced Renal Injury.
Pruritus
Acquired Angioedema: A Rare Manifestation of Angioimmunoblastic T Cell Lymphoma.
Pruritus
Hereditary angioedema as a cause of transient abdominal pain.
Psoriasis
Functional MASP2 single nucleotide polymorphism plays no role in psoriasis.
Pulmonary Disease, Chronic Obstructive
MASPs at the crossroad between the complement and the coagulation cascades - the case for COVID-19.
Purpura
Helicobacter pylori infection and skin diseases.
Purpura, Thrombocytopenic, Idiopathic
Lupus anticoagulant and thrombosis in splenic marginal zone lymphoma.
Renal Insufficiency, Chronic
MASPs at the crossroad between the complement and the coagulation cascades - the case for COVID-19.
Renal Insufficiency, Chronic
The Inhibition of Complement System in Formal and Emerging Indications: Results from Parallel One-Stage Pairwise and Network Meta-Analyses of Clinical Trials and Real-Life Data Studies.
Reperfusion Injury
A novel series of arylsulfonylthiophene-2-carboxamidine inhibitors of the complement component C1s.
Reperfusion Injury
Administration of C1-esterase inhibitor during emergency coronary artery bypass surgery in acute ST-elevation myocardial infarction.
Reperfusion Injury
Apotransferrin, C1-esterase inhibitor, and alpha 1-acid glycoprotein for cerebral protection during experimental hypothermic circulatory arrest.
Reperfusion Injury
C1 esterase inhibitor ameliorates ischemia reperfusion injury in a swine musculocutaneous flap model.
Reperfusion Injury
C1 esterase inhibitor reduces lower extremity ischemia/reperfusion injury and associated lung damage.
Reperfusion Injury
C1-esterase inhibitor reduces reperfusion injury after lung transplantation.
Reperfusion Injury
C1-esterase inhibitor reverses functional consequences of superior mesenteric artery ischemia/reperfusion by limiting reperfusion injury and restoring microcirculatory perfusion.
Reperfusion Injury
Design and synthesis of polyethylene glycol-modified biphenylsulfonyl-thiophene-carboxamidine inhibitors of the complement component C1s.
Reperfusion Injury
Effects of Ischemic Preconditioning and C1 Esterase Inhibitor Administration following Ischemia-Reperfusion Injury in a Rat Skin Flap Model.
Reperfusion Injury
Intracoronary application of C1 esterase inhibitor improves cardiac function and reduces myocardial necrosis in an experimental model of ischemia and reperfusion.
Reperfusion Injury
Mannan binding lectin-associated serine protease-2 (MASP-2) critically contributes to post-ischemic brain injury independent of MASP-1.
Reperfusion Injury
Protective effect of C1 esterase inhibitor on reperfusion injury in the rat middle cerebral artery occlusion model.
Reperfusion Injury
Single-lung transplantation in a patient with cystic fibrosis and an asymmetric thorax.
Reperfusion Injury
Targeting of mannan-binding lectin-associated serine protease-2 confers protection from myocardial and gastrointestinal ischemia/reperfusion injury.
Reperfusion Injury
Three-Year Outcomes of a Randomized, Double-Blind, Placebo-Controlled Study Assessing Safety and Efficacy of C1 Esterase Inhibitor for Prevention of Delayed Graft Function in Deceased Donor Kidney Transplant Recipients.
Respiratory Distress Syndrome
Design and synthesis of polyethylene glycol-modified biphenylsulfonyl-thiophene-carboxamidine inhibitors of the complement component C1s.
Respiratory Insufficiency
Successful use of daily intravenous infusion of C1 esterase inhibitor concentrate in the treatment of a hereditary angioedema patient with ascites, hypovolemic shock, sepsis, renal and respiratory failure.
Rheumatic Diseases
Trimer and tetramer complexes containing C1 esterase inhibitor, C1r and C1s, in serum and synovial fluid of patients with rheumatic disease.
Rheumatic Fever
Association of MASP2 polymorphisms and protein levels with rheumatic fever and rheumatic heart disease.
Rheumatic Fever
Functional MASP2 gene polymorphism in patients with history of rheumatic fever.
Rheumatic Heart Disease
Association of MASP2 polymorphisms and protein levels with rheumatic fever and rheumatic heart disease.
Rheumatic Heart Disease
Functional MASP2 gene polymorphism in patients with history of rheumatic fever.
Rosacea
Helicobacter pylori infection and skin diseases.
Schistosomiasis haematobia
Low MBL-associated serine protease 2 (MASP-2) levels correlate with urogenital schistosomiasis in Nigerian children.
Scleroderma, Systemic
Helicobacter pylori infection and skin diseases.
Sepsis
Bench-to-bedside review: The role of C1-esterase inhibitor in sepsis and other critical illnesses.
Sepsis
C1-esterase inhibitor and its effects on endotoxin-induced leukocyte adherence and plasma extravasation in postcapillary venules.
Sepsis
C1-esterase inhibitor attenuates the inflammatory response during human endotoxemia.
Sepsis
C1-esterase inhibitor in early septicemia.
Sepsis
C1-esterase inhibitor infusion increases survival rates for patients with sepsis*
Sepsis
C1-esterase inhibitor substitution in sepsis.
Sepsis
Components of the lectin pathway of complement activation in paediatric patients of intensive care units.
Sepsis
Plasma kallikrein-kinin system in patients with uncomplicated sepsis and septic shock--comparison with cardiogenic shock.
Sepsis
Successful use of daily intravenous infusion of C1 esterase inhibitor concentrate in the treatment of a hereditary angioedema patient with ascites, hypovolemic shock, sepsis, renal and respiratory failure.
Sepsis
[Safety and efficacy of purified human C1-esterase inhibitor in the treatment of patients with sepsis]
Severe Acute Respiratory Syndrome
C1 esterase inhibitor and the contact system in COVID-19.
Shock, Septic
Combined antithrombin III and C1-esterase inhibitor treatment decreases intravascular fibrin deposition and attenuates cardiorespiratory impairment in rabbits exposed to Escherichia coli endotoxin.
Shock, Septic
Cysteine proteinase from Streptococcus pyogenes enables evasion of innate immunity via degradation of complement factors.
Shock, Septic
Initial studies on the administration of C1-esterase inhibitor to patients with septic shock or with a vascular leak syndrome induced by interleukin-2 therapy.
Shock, Septic
Plasma kallikrein-kinin system in patients with uncomplicated sepsis and septic shock--comparison with cardiogenic shock.
Shock, Septic
Septic shock after liver transplantation for Caroli's disease: clinical improvement after treatment with C1-esterase inhibitor.
Shock, Septic
Studies on components of the plasma kallikrein-kinin system in plasma samples from normal individuals and patients with septic shock.
Shock, Septic
The effect of C1-esterase inhibitor in definite and suspected streptococcal toxic shock syndrome. Report of seven patients.
Shock, Septic
The role of complement system in septic shock.
Skin Diseases
Helicobacter pylori infection and skin diseases.
Spinal Cord Injuries
Protective effect of C1 esterase inhibitor on acute traumatic spinal cord injury in the rat.
Sporotrichosis
Mannose-Binding Lectin and MBL-Associated Serine Protease-2 Genotypes and Serum Levels in Patients with Sporotrichosis.
Status Epilepticus
Early treatment with C1 esterase inhibitor improves weight but not memory deficits in a rat model of status epilepticus.
Stroke
Genetically-defined deficiency of mannose-binding lectin is associated with protection after experimental stroke in mice and outcome in human stroke.
Stroke
Mannan binding lectin-associated serine protease-2 (MASP-2) critically contributes to post-ischemic brain injury independent of MASP-1.
Stroke
Outcomes of long term treatments of type I hereditary angioedema in a Turkish family.
Stroke
Plasma levels of mannan-binding lectin (MBL)-associated serine proteases (MASPs) and MBL-associated protein in cardio- and cerebrovascular diseases.
Stroke
TFPI inhibits lectin pathway of complement activation by direct interaction with MASP-2.
Subarachnoid Hemorrhage
Human brain trauma severity is associated with lectin complement pathway activation.
Sweet Syndrome
Helicobacter pylori infection and skin diseases.
Thrombophilia
Proteomic analysis of plasma from children with sickle cell anemia and silent cerebral infarction.
Thrombophilia
The influence of C1-esterase inhibitor substitution on coagulation and cardiorespiratory parameters in an endotoxin-induced rabbit model of hypercoagulability.
Thrombosis
Assessment of hereditary angioedema treatment risks.
Thrombosis
C1-esterase inhibitor enhances thrombin generation and spatial fibrin clot propagation in the presence of thrombomodulin.
Thrombosis
Hypersensitive mousetraps, alpha1-antitrypsin deficiency and dementia.
Thrombosis
Plasma levels of mannan-binding lectin (MBL)-associated serine proteases (MASPs) and MBL-associated protein in cardio- and cerebrovascular diseases.
Thrombotic Microangiopathies
The Inhibition of Complement System in Formal and Emerging Indications: Results from Parallel One-Stage Pairwise and Network Meta-Analyses of Clinical Trials and Real-Life Data Studies.
Tuberculosis
Construction of human MASP-2-CCP1/2SP, CCP2SP, SP plasmid DNA nanolipoplexes and the effects on tuberculosis in BCG-infected mice.
Tuberculosis
Effects of hMASP-2 on the formation of BCG infection-induced granuloma in the lungs of BALB/c mice.
Tuberculosis
Effects of MBL-associated serine protease-2 (MASP-2) on liquefaction and ulceration in rabbit skin model of tuberculosis.
Tuberculosis
Impact of MBL and MASP-2 gene polymorphism and its interaction on susceptibility to tuberculosis.
Tuberculosis
Tuberculosis, onychomycosis and immune deficiency in complicated Crohn's disease.
Tuberculosis, Pulmonary
No Strong Relationship Between Components of the Lectin Pathway of Complement and Susceptibility to Pulmonary Tuberculosis.
Urticaria
Allergic urticaria and hereditary angioedema. Independent association in the same patient.
Urticaria
An update on the diagnosis and management of hereditary angioedema with abnormal c1 inhibitor.
Urticaria
Angioedema due to Systemic Isotretinoin Therapy.
Urticaria
Angioedema suppressed by a combination of anti-histamine and leukotriene modifier.
Urticaria
Exogenous oestrogen as an alternative to food allergy in the aetiology of angioneurotic oedema.
Urticaria
Hereditary angioedema as a cause of transient abdominal pain.
Urticaria
Intractable acquired autoimmune angioedema in a patient with systemic lupus erythematosus.
Urticaria
Monoclonal gammopathy in association with allergic disorders of the skin and respiratory tract.
Urticaria
On the role of the C1-esterase inhibitor in cold urticaria.
Urticaria
Protease inhibitors in plasma of patients with chronic urticaria.
Urticaria
The value of C1 esterase inhibitor in patients with aspirin-sensitive urticaria.
Urticaria
[Behavior of esterase inhibitor C1 in patients with urticaria due to aspirin hypersensitivity]
Uterine Cervical Neoplasms
MASP-1 and MASP-2 Serum Levels Are Associated With Worse Prognostic in Cervical Cancer Progression.
Uterine Inertia
Reference range for C1-esterase inhibitor (C1 INH) in the third trimester of pregnancy.
Vasculitis
Angiooedema due to acquired deficiency of C1-esterase inhibitor associated with leucocytoclastic vasculitis.
Vasculitis
Experimentally-induced anti-myeloperoxidase vasculitis does not require properdin, MASP-2 or bone marrow-derived C5.
Vasculitis
Monoclonal gammopathy with significance: case series and literature review.
Vasculitis
Urticarial vasculitis and asymptomatic acquired C1 esterase inhibitor deficiency revealing an angioimmunoblastic T cell lymphoma.
Vasculitis
Urticarial vasculitis in a connective tissue disease clinic: patterns, presentations, and treatment.
Vasculitis
Urticarial vasculitis, IgA deficiency and C1 esterase inhibitor deficiency in the presence of an IgG monoclonal gammopathy--a case report.
Vocal Cord Paralysis
[Croup syndrome]
Whooping Cough
Bordetella pertussis autotransporter Vag8 binds human C1 esterase inhibitor and confers serum resistance.
Whooping Cough
Bordetella pertussis binds human C1 esterase inhibitor during the virulent phase, to evade complement-mediated killing.
Xanthomatosis
Unusual normolipidemic cutaneous xanthomatosis: a comparison of two cases illustrating the differential diagnosis.
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3.4.21.42 complement subcomponent C1s
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The reliability class of the localization prediction ranges from 1 (very reliable) to 5 (not reliable). 
