Reference on EC 1.1.1.211 - long-chain-3-hydroxyacyl-CoA dehydrogenase

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REF.
AUTHORS
TITLE
JOURNAL
VOL.
PAGES
YEAR
ORGANISM (UNIPROT)
PUBMED ID
SOURCE
El-Fakhri, M.; Middleton, B.
The existence of an inner-membrane-bound, long acyl-chain-specific 3-hydroxyacyl-CoA dehydrogenase in mammalian mitochondria
Biochim. Biophys. Acta
713
270-279
1982
Oryctolagus cuniculus, Rattus norvegicus
Manually annotated by BRENDA team
Carpenter, K.; Pollitt, R.J.; Middleton, B.
Human liver long-chain 3-hydroxyacyl-coenzyme A dehydrogenase is a multifunctional membrane-bound beta-oxidation enzyme of mitochondria
Biochem. Biophys. Res. Commun.
183
443 - 448
1992
Homo sapiens
Manually annotated by BRENDA team
Middleton, B.
The mitochondrial long-chain trifunctional enzyme: 2-enoyl-CoA hydratase, 3-hydroxyacyl-CoA dehydrogenase and 3-oxoacyl-CoA thiolase
Biochem. Soc. Trans.
22
427-431
1994
Homo sapiens
Manually annotated by BRENDA team
Uchida, Y.; Izai, K.; Orii, T.; Hashimoto, T.
Novel fatty acid beta-oxidation enzymes in rat liver mitochondria. II. Purification and properties of enoyl-coenzyme A (CoA) hydratase/3-hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase trifunctional protein
J. Biol. Chem.
267
1034-1041
1992
Rattus norvegicus (Q64428)
Manually annotated by BRENDA team
Carpenter, K.; Pollitt, R.J.; Middleton, B.
A unique, membrane-bound, multifunctional enzyme from human liver mitochondria catalysing three steps of fatty acid beta-oxidation
Biochem. Soc. Trans.
21
35S
1992
Homo sapiens
Manually annotated by BRENDA team
Jones, P.M.; Butt, Y.M.; Bennett, M.J.
Effects of odd-numbered medium-chain fatty acids on the accumulation of long-chain 3-hydroxy-fatty acids in long-chain L-3-hydroxyacyl CoA dehydrogenase and mitochondrial trifunctional protein deficient skin fibroblasts
Mol. Genet. Metab.
81
96-99
2004
Homo sapiens
Manually annotated by BRENDA team
Rakheja, D.; Bennett, M.J.; Foster, B.M.; Domiati-Saad, R.; Rogers, B.B.
Evidence for fatty acid oxidation in human placenta, and the relationship of fatty acid oxidation enzyme activities with gestational age
Placenta
23
447-450
2002
Homo sapiens
Manually annotated by BRENDA team
Gillingham, M.B.; Weleber, R.G.; Neuringer, M.; Connor, W.E.; Mills, M.; van Calcar, S.; Ver Hoeve, J.; Wolff, J.; Harding, C.O.
Effect of optimal dietary therapy upon visual function in children with long-chain 3-hydroxyacyl CoA dehydrogenase and trifunctional protein deficiency
Mol. Genet. Metab.
86
124-133
2005
Homo sapiens
Manually annotated by BRENDA team
Oey, N.A.; den Boer, M.E.; Wijburg, F.A.; Vekemans, M.; Auge, J.; Steiner, C.; Wanders, R.J.; Waterham, H.R.; Ruiter, J.P.; Attie-Bitach, T.
Long-chain fatty acid oxidation during early human development
Pediatr. Res.
57
755-759
2005
Homo sapiens
Manually annotated by BRENDA team
Law, L.K.; Tang, N.L.; Hui, J.; Ho, C.S.; Ruiter, J.; Fok, T.F.; Wanders, R.J.; Lam, C.W.
A novel functional assay for simultaneous determination of total fatty acid beta-oxidation flux and acylcarnitine profiling in human skin fibroblasts using (2)H(31)-palmitate by isotope ratio mass spectrometry and electrospray tandem mass spectrometry
Clin. Chim. Acta
382
25-30
2007
Homo sapiens
Manually annotated by BRENDA team
Kong, X.F.; Zhang, X.X.; Yu, Y.Y.; Shi, Q.; La, D.D.; Zhu-Ge, C.D.; Deng, L.; Gong, Q.M.; Shen, B.Y.; Peng, C.H.; Li, H.W.
No mutation was found in the alpha-subunit of the mitochondrial tri-functional protein in one patient with severe acute fatty liver of pregnancy and her relatives
J. Gastroenterol. Hepatol.
22
2107-2111
2007
Homo sapiens
Manually annotated by BRENDA team
Ma, L.; Zhang, H.; Liu, Q.; Chen, J.; Zhang, J.; Chen, G.Q.
Production of two monomer structures containing medium-chain-length polyhydroxyalkanoates by beta-oxidation-impaired mutant of Pseudomonas putida KT2442
Biores. Technol.
100
4891-4894
2009
Pseudomonas putida (Q88L88), Pseudomonas putida KT2442 (Q88L88)
Manually annotated by BRENDA team
Park, H.D.; Kim, S.R.; Ki, C.S.; Lee, S.Y.; Chang, Y.S.; Jin, D.K.; Park, W.S.
Two novel HADHB gene mutations in a Korean patient with mitochondrial trifunctional protein deficiency
Ann. Clin. Lab. Sci.
39
399-404
2009
Homo sapiens
Manually annotated by BRENDA team
Griffin, A.C.; Strauss, A.W.; Bennett, M.J.; Ernst, L.M.
Mutations in long-chain 3-hydroxyacyl coenzyme A dehydrogenase are associated with placental maternal floor infarction/massive perivillous fibrin deposition
Pediatr. Dev. Pathol.
15
368-374
2012
Homo sapiens
Manually annotated by BRENDA team