Please wait a moment until all data is loaded. This message will disappear when all data is loaded.
Please wait a moment until the data is sorted. This message will disappear when the data is sorted.
2 ATP + L-Gln + HCO3-
2 ADP + phosphate + L-Glu + carbamoyl phosphate
2 ATP + NH3 + CO2 + H2O
2 ADP + phosphate + carbamoyl phosphate
2 ATP + NH3 + CO2 + H2O
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
ATP + carbamate
ADP + carbamoyl phosphate
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoylphosphate
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
ATP + NH4+ + HCO3- + H2O
ADP + phosphate + carbamoyl phosphate
additional information
?
-
2 ATP + L-Gln + HCO3-
2 ADP + phosphate + L-Glu + carbamoyl phosphate
-
-
-
?
2 ATP + L-Gln + HCO3-
2 ADP + phosphate + L-Glu + carbamoyl phosphate
-
-
-
?
2 ATP + NH3 + CO2 + H2O
2 ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
2 ATP + NH3 + CO2 + H2O
2 ADP + phosphate + carbamoyl phosphate
-
-
-
?
2 ATP + NH3 + CO2 + H2O
2 ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
2 ATP + NH3 + CO2 + H2O
2 ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
2 ATP + NH3 + CO2 + H2O
2 ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
2 ATP + NH3 + CO2 + H2O
2 ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
2 ATP + NH3 + CO2 + H2O
?
-
plays a key role in the regulation of the urea cycle
-
-
?
2 ATP + NH3 + CO2 + H2O
?
-
primary ammonia-detoxifying enzyme
-
-
?
2 ATP + NH3 + CO2 + H2O
?
-
enzyme is involved in arginine and urea synthesis
-
-
?
2 ATP + NH3 + CO2 + H2O
?
-
primary ammonia-detoxifying enzyme
-
-
?
2 ATP + NH3 + CO2 + H2O
?
-
-
-
-
?
2 ATP + NH3 + CO2 + H2O
?
-
first enzyme involved in the biosynthesis of urea in the liver ureotelic animals
-
-
?
2 ATP + NH3 + CO2 + H2O
?
-
enzyme of urea cycle
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
ATP in form of MgATP2-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
ATP in form of CoATP2-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
ATP in form of MgATP2-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
ATP in form of MnATP2-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
ATP in form of MgATP2-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
ATP in form of CoATP2-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
?
2 ATP + NH4+ + HCO3-
2 ADP + phosphate + carbamoyl phosphate
-
-
-
?
ATP + carbamate
ADP + carbamoyl phosphate
-
-
r
ATP + carbamate
ADP + carbamoyl phosphate
-
-
-
r
ATP + carbamate
ADP + carbamoyl phosphate
-
-
-
r
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
first step of the both the urea cycle and pyrimidine nucleotide biosynthesis patways
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
ir
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
ir
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
the enzyme T1405N genotype influences nitric oxide production as well as vascular smooth muscle reactivity
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
CPS1 is a rate-limiting enzyme in the urea cycle
-
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
three step reaction
-
ir
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
ir
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
three step reaction
-
ir
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
the first and rate-limiting step of the urea synthesis
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
enzyme of the urea cycle
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
CPS is the rate-determining enzyme of the urea cycle and catalyzes the conversion of ammonia and bicarbonate to carbamoylphosphate in the periportal and intermediate zones of a liver lobule, overview. The enzyme is responsible for ammonia elimination
-
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
-
?
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
the product carbamoyl phosphate is used in the biosynthesis of pyrimidines, arginine, and urea
-
ir
ATP + NH3 + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
the product carbamoylphosphate is used in the biosynethsis of pyrimidines, arginine, and urea
-
ir
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
Frog
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
no activity with Gln
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
no activity with Gln
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
no activity with Gln
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
no activity with Gln
-
?
ATP + NH4+ + CO2 + H2O
ADP + phosphate + carbamoylphosphate
-
-
-
?
ATP + NH4+ + HCO3- + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
?
ATP + NH4+ + HCO3- + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
-
?
ATP + NH4+ + HCO3- + H2O
ADP + phosphate + carbamoyl phosphate
the human enzyme removes excess, potentially neurotoxic ammonia via the urea cycle in a tightly regulated manner that avoids depletion of the ammonia pool, and shows inability to use glutamine as an alternative nitrogen donor
-
-
?
ATP + NH4+ + HCO3- + H2O
ADP + phosphate + carbamoyl phosphate
synthesis of carbamoyl phosphate requires coordination of two hCPS active sites with ATP cleavage occurring at duplicated ATP grasp domains B and C
-
-
?
ATP + NH4+ + HCO3- + H2O
ADP + phosphate + carbamoyl phosphate
-
-
-
?
additional information
?
-
-
Rana cancrivora up-regulates hepatic carbamoyl phosphate synthetase I activity and tissue osmolyte levels in response to increased salinity
-
-
?
additional information
?
-
-
polymorphism of carbamyl phosphate synthetase I, certain carbamyl phosphate synthetase I alleles are associated with clinical outcome
-
-
?
additional information
?
-
the enzyme might play an important role in spermiogenesis
-
-
?
additional information
?
-
-
the enzyme might play an important role in spermiogenesis
-
-
?
additional information
?
-
severe hyperammonaemia and high mortality are observed in hCPS deficiency, a rare autosomal disease
-
-
?
additional information
?
-
-
severe hyperammonaemia and high mortality are observed in hCPS deficiency, a rare autosomal disease
-
-
?
additional information
?
-
-
this enzyme is unable to bind and utilize L-glutamine
-
?