3.2.1.76: L-iduronidase
This is an abbreviated version!
For detailed information about L-iduronidase, go to the full flat file.
Word Map on EC 3.2.1.76
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3.2.1.76
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mucopolysaccharidosis
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lysosomal
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hurler
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glycosaminoglycans
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scheie
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dermatan
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heparan
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hurler-scheie
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hematopoietic
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corneal
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medicine
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mucopolysaccharide
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intrathecal
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clouding
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hepatosplenomegaly
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iduronate
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pompe
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pharmacology
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enzyme-replacement
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4-methylumbelliferyl
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facies
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mckusick
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diagnostics
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dysostosis
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fabry
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drug development
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gaucher
- 3.2.1.76
- mucopolysaccharidosis
- lysosomal
- hurler
- glycosaminoglycans
-
scheie
- dermatan
- heparan
-
hurler-scheie
-
hematopoietic
- corneal
- medicine
-
mucopolysaccharide
-
intrathecal
-
clouding
-
hepatosplenomegaly
-
iduronate
- pompe
- pharmacology
-
enzyme-replacement
-
4-methylumbelliferyl
-
facies
-
mckusick
- diagnostics
-
dysostosis
- fabry
- drug development
- gaucher
Reaction
Synonyms
Aldurazyme, alpha-IDUA, alpha-iduronidase, alpha-L-iduronidase, alpha-L-iduronidase A, glycosaminoglycan alpha-L-iduronohydrolase, hIDUA, IDU, IDUA, iduronidase, laronidase, More, rIDUA_RLT
ECTree
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Specific Activity
Specific Activity on EC 3.2.1.76 - L-iduronidase
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0.0000014 - 0.000027
mucopolysaccharidosis type I mutant enzymes, immunocapture-enriched from skin fibroblast
0.000005 - 0.00011
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activity levels from the same specimens of heterozygous mice vary greatly with different substrate concentrations of 4-methylumbelliferyl-alpha-L-iduronide, comparison of activities in livers at 15 different concentrations, overview. pH and temperature not specified in the publication
0.00003 - 0.000093
wild-type enzyme, immunocapture-enriched from skin fibroblast
0.0029
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recombinant enzyme, using 4-methylumbelliferyl-alpha-L-iduronide as a substrate
0.0033 - 0.0053
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wild-type cell lines, pH not specified in the publication, 37°C
0.018
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native enzyme, using 4-methylumbelliferyl-alpha-L-iduronide as a substrate
0.03
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recombinant enzyme, using 4-methylumbelliferyl-alpha-L-iduronide as a substrate
additional information
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specific activity in healthy individuals was found to be higher than specific activity in mucopolysaccharidosis patients group I but similar with mucopolysaccharidosis patients group II