3.2.1.50: alpha-N-acetylglucosaminidase
This is an abbreviated version!
For detailed information about alpha-N-acetylglucosaminidase, go to the full flat file.
Word Map on EC 3.2.1.50
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3.2.1.50
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oligosaccharide
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glycoside
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lysosomal
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glycans
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n-linked
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lectin
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beta-glucosidase
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sialic
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neuraminidase
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glycoconjugates
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n-acetylglucosamine
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iminosugars
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glycopeptides
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sialylated
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glcnac
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alpha-l-fucosidase
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mucopolysaccharidosis
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sialidase
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anomeric
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polyhydroxylated
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swainsonine
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mannosidase
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1-deoxynojirimycin
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asparagine-linked
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fucosylated
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high-mannose
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beta-n-acetylglucosaminidase
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beta-d-galactosidase
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naglu
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complex-type
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alpha-d-mannosidase
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1-deoxymannojirimycin
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fucosidase
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alpha-d-galactosidase
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n-acetyl-beta-d-glucosaminidase
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almond
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transglycosylation
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pngase
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hydrazinolysis
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castanospermine
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sulfonium
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alpha-n-acetylgalactosaminidase
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beta-d-xylosidase
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neuac
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mannose-type
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triantennary
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endo-beta-galactosidase
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beta-mannosidase
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alpha-d-glucosidase
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alpha-l-iduronidase
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medicine
- 3.2.1.50
- oligosaccharide
- glycoside
- lysosomal
- glycans
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n-linked
- lectin
- beta-glucosidase
-
sialic
- neuraminidase
- glycoconjugates
- n-acetylglucosamine
-
iminosugars
- glycopeptides
-
sialylated
- glcnac
- alpha-l-fucosidase
- mucopolysaccharidosis
- sialidase
-
anomeric
-
polyhydroxylated
- swainsonine
-
mannosidase
- 1-deoxynojirimycin
-
asparagine-linked
-
fucosylated
-
high-mannose
- beta-n-acetylglucosaminidase
- beta-d-galactosidase
- naglu
-
complex-type
- alpha-d-mannosidase
- 1-deoxymannojirimycin
-
fucosidase
- alpha-d-galactosidase
-
n-acetyl-beta-d-glucosaminidase
- almond
-
transglycosylation
-
pngase
-
hydrazinolysis
- castanospermine
-
sulfonium
- alpha-n-acetylgalactosaminidase
- beta-d-xylosidase
- neuac
-
mannose-type
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triantennary
- endo-beta-galactosidase
- beta-mannosidase
- alpha-d-glucosidase
- alpha-l-iduronidase
- medicine
Reaction
Synonyms
2-acetamido-2-deoxy-alpha-D-glucoside acetamidodeoxyglucohydrolase, AgnB, AgnC, alpha-acetylglucosaminidase, alpha-N-acetylglucosaminidase, BMN 250, exo-glycosidase, glycosidase, heparan N-sulfatase, N-acetyl-alpha-D-glucosaminidase, N-acetyl-alpha-glucosaminidase, NAG, NAGase, NAGLU, Sanfilippo b corrective factor
ECTree
3.2.1.50 alpha-N-acetylglucosaminidaseAdvanced search results
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results (Natural Substrates Products
Natural Substrates Products on EC 3.2.1.50 - alpha-N-acetylglucosaminidase
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NATURAL SUBSTRATE 
NATURAL PRODUCT
REACTION DIAGRAM
ORGANISM
UNIPROT
COMMENTARY
(Substrate)
(Substrate)
LITERATURE
(Substrate)
(Substrate)
COMMENTARY
(Product)
(Product)
LITERATURE
(Product)
(Product)
REVERSIBILITY
r=reversible
ir=irreversible
?=not specified
r=reversible
ir=irreversible
?=not specified
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
UDP-N-acetyl-alpha-D-glucosamine + H2O
uridine-5'-diphosphate + N-acetyl-alpha-D-glucosamine
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-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
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involved in the degradation of heparin and heparan sulfate
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
involved in the degradation of heparin and heparan sulfate
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
involved in the degradation of heparin and heparan sulfate
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
involved in the degradation of heparin and heparan sulfate
-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
involved in the degradation of heparin and heparan sulfate
-
-
?
(GlcNAcalpha(1-4))n + H2O
(GlcNAcalpha(1-4))n-1 + 2-(acetylamino)-2-deoxy-beta-D-glucopyranose
-
-
-
?
additional information
?
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mucopolysaccharidosis type IIIB is a lysosomal storage disorder characterized by the defective degradation of heparan sulfate due to a deficiency of alpha-N-acetylglucosaminidase. The clinical severity of mucopolysacchariddosis type IIIB ranges from an attenuated to severely affected Sanfilippo phenotype. Relationship between genotype, cellular biochemistry and clinical phenotype in a F48L/R297X compound heterozygous mucopolysaccharidosis type IIIB patient with an attenuated Sanfilippo phenotype
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?
additional information
?
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enzyme deficiency causes the Sanfilippo type B syndrome, i.e. the mucopolysaccharidosis type IIIB, a lysosomal storage disorder, phenotype, overview
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?
additional information
?
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enzyme deficiency causes the Sanfilippo type B syndrome, i.e. the mucopolysaccharidosis type IIIB, an autosomal recessive lysosomal storage disorder, overview
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?
